OTTOBONI, LINDA
OTTOBONI, LINDA
Dipartimento di Fisiopatologia Medico-Chirurgica e dei Trapianti
RNA biomarkers in spinal muscular atrophy: enhancing pathogenesis understanding and guiding precision medicine
2026 C. Alberti, A. Berardinelli, G.P. Comi, L. Ottoboni, S. Corti
Skeletal muscle in spinal muscular atrophy: Critical insights from pathogenesis to therapeutic strategies
2026 L. Ottoboni, C. Panicucci, G. Magni, D. Gagliardi, M. Ripolone, L. Napoli, M. Moggio, G.P. Comi, C. Bruno, S.P. Corti
Advances and challenges in modeling Charcot-Marie-Tooth type 2A using iPSC-derived models
2025 M. Rizzuti, E. Pagliari, M. D'Agostino, L. Ottoboni, V. Parente, G.P. Comi, S. Corti, F. Rizzo, E. Abati
Decoding inflammatory pathways in spinal muscular atrophy: implications for next-generation therapies
2025 L. Ottoboni, C. Bruno, S. Corti
TDP-43 Regulates Rab4 Levels to Support Synaptic Vesicle Recycling and Neuromuscular Connectivity in Drosophila and Human ALS Models
2025 M. Gbadamosi, G. Romano, M. Simbula, G. Canarutto, L. Ottoboni, S. Corti, F. Feiguin
Statistical characterization of cortical–thalamic dynamics evoked by cortical stimulation in mice
2025 D. Nigrisoli, S. Russo, R. Freddi, N. Seseri, S. Corti, L. Ottoboni, R. Barbieri
Transplanted human striatal progenitors exhibit functional integration and modulate host circuitry in a Huntington’s disease animal model
2025 L. Scaramuzza, M. Ribodino, C. Cassarino, M. Morrocchi, G.B. Gomez Gonzalez, R. Parolisi, E. Sozzi, G. Turrini, V. Cerrato, P. Conforti, E. Hoxha, R. Tognato, G. Galeotti, C. Cordiglieri, M.C. Crosti, S. Zucca, M. Lorenzati, S. Bovetti, P. Spaiardi, C. De'Sperati, G. Biella, L. Ottoboni, M. Parmar, S. Maestri, D. Besusso, E. Cattaneo, A. Buffo
Single Nucleotide SMN1 Variants in a Cohort of Individuals With Spinal Muscular Atrophy
2025 M. Rimoldi, F. Magri, M. Meneri, D. Gagliardi, V. Ada Sansone, E. Albamonte, L. Ottoboni, G.P. Comi, E. Mercuri, F.D. Tiziano, D. Ronchi, S. Corti
C9orf72 Repeat Expansion Induces Metabolic Dysfunction in Human iPSC‐Derived Microglia and Modulates Glial‐Neuronal Crosstalk
2025 M. Mearelli, I. Hirschberg, C. Weissleder, C. Giachino, M.J. Pérez, M. Dubroux, F. Provenzano, M. Rizzuti, L. Ottoboni, U. Sheth, T.F. Gendron, S. Corti, M. Deleidi
Advancing personalized spinal muscular atrophy care: matching the right biomarker to the right patient at the right time
2025 S. Corti, L. Ottoboni, V. Sansone
Unleashing the potential of mRNA therapeutics for inherited neurological diseases
2024 E. Monfrini, G. Baso, D. Ronchi, M. Meneri, D. Gagliardi, L. Quetti, F. Verde, N. Ticozzi, A. Ratti, A. Di Fonzo, G.P. Comi, L. Ottoboni, S. Corti
Shaping the Neurovascular Unit Exploiting Human Brain Organoids
2024 M. Rizzuti, V. Melzi, L. Brambilla, L. Quetti, L. Sali, L. Ottoboni, M. Meneri, A. Ratti, F. Verde, N. Ticozzi, G.P. Comi, S. Corti, E. Abati
Improved synthesis and application of an alkyne-functionalized isoprenoid analogue to study the prenylomes of motor neurons, astrocytes and their stem cell progenitors
2024 K.F. Suazo, V. Mishra, S. Maity, S.A. Auger, K. Justyna, A.M. Petre, L. Ottoboni, J. Ongaro, S.P. Corti, F. Lotti, S. Przedborski, M.D. Distefano
Heparin Precursors with Reduced Anticoagulant Properties Retain Antiviral and Protective Effects That Potentiate the Efficacy of Sofosbuvir against Zika Virus Infection in Human Neural Progenitor Cells
2023 I. Pagani, L. Ottoboni, P. Panina-Bordignon, G. Martino, G. Poli, S. Taylor, J.E. Turnbull, E. Yates, E. Vicenzi
Combined RNA interference and gene replacement therapy targeting MFN2 as proof of principle for the treatment of Charcot-Marie-Tooth type 2A
2023 F. Rizzo, S. Bono, M.D. Ruepp, S. Salani, L. Ottoboni, E. Abati, V. Melzi, C. Cordiglieri, S. Pagliarani, R. De Gioia, A. Anastasia, M. Taiana, M. Garbellini, S. Lodato, P. Kunderfranco, D. Cazzato, D. Cartelli, C. Lonati, N. Bresolin, G. Comi, M. Nizzardo, S. Corti
iAstrocytes do not restrain T cell proliferation in vitro
2023 E. Colombo, A. De Angelis, C. Bassani, F. Ruffini, L. Ottoboni, L. Garzetti, A. Finardi, G. Martino, R. Furlan, C. Farina
Genomic and transcriptomic advances in amyotrophic lateral sclerosis
2023 M. Rizzuti, L. Sali, V. Melzi, S. Scarcella, G. Costamagna, L. Ottoboni, L. Quetti, L. Brambilla, D. Papadimitriou, F. Verde, A. Ratti, N. Ticozzi, G.P. Comi, S. Corti, D. Gagliardi
Neural stem cell transplantation in patients with progressive multiple sclerosis: an open-label, phase 1 study
2023 A. Genchi, E. Brambilla, F. Sangalli, M. Radaelli, M. Bacigaluppi, R. Furlan, A. Andolfo, D. Drago, C. Magagnotti, G.M. Scotti, R. Greco, P. Vezzulli, L. Ottoboni, M. Bonopane, D. Capilupo, F. Ruffini, D. Belotti, B. Cabiati, S. Cesana, G. Matera, L. Leocani, V. Martinelli, L. Moiola, L. Vago, P. Panina-Bordignon, A. Falini, F. Ciceri, A. Uglietti, M.P. Sormani, G. Comi, M.A. Battaglia, M.A. Rocca, L. Storelli, E. Pagani, G. Gaipa, G. Martino
Multi-omics profiling of CSF from spinal muscular atrophy type 3 patients after nusinersen treatment: a 2-year follow-up multicenter retrospective study
2023 I. Faravelli, D. Gagliardi, E. Abati, M. Meneri, J. Ongaro, F. Magri, V. Parente, L. Petrozzi, G. Ricci, F. Farè, G. Garrone, M. Fontana, D. Caruso, G. Siciliano, G.P. Comi, A. Govoni, S. Corti, L. Ottoboni
Identification of Novel Biomarkers of Spinal Muscular Atrophy and Therapeutic Response by Proteomic and Metabolomic Profiling of Human Biological Fluid Samples
2023 M. Meneri, E. Abati, D. Gagliardi, I. Faravelli, V. Parente, A. Ratti, F. Verde, N. Ticozzi, G.P. Comi, L. Ottoboni, S. Corti