OTTOBONI, LINDA
OTTOBONI, LINDA
Dipartimento di Fisiopatologia Medico-Chirurgica e dei Trapianti
Decoding inflammatory pathways in spinal muscular atrophy: implications for next-generation therapies
2025 L. Ottoboni, C. Bruno, S. Corti
Single Nucleotide SMN1 Variants in a Cohort of Individuals With Spinal Muscular Atrophy
2025 M. Rimoldi, F. Magri, M. Meneri, D. Gagliardi, V. Ada Sansone, E. Albamonte, L. Ottoboni, G.P. Comi, E. Mercuri, F.D. Tiziano, D. Ronchi, S. Corti
Advances and challenges in modeling Charcot-Marie-Tooth type 2A using iPSC-derived models
2025 M. Rizzuti, E. Pagliari, M. D'Agostino, L. Ottoboni, V. Parente, G.P. Comi, S. Corti, F. Rizzo, E. Abati
Statistical characterization of cortical–thalamic dynamics evoked by cortical stimulation in mice
2025 D. Nigrisoli, S. Russo, R. Freddi, N. Seseri, S. Corti, L. Ottoboni, R. Barbieri
Advancing personalized spinal muscular atrophy care: matching the right biomarker to the right patient at the right time
2025 S. Corti, L. Ottoboni, V. Sansone
TDP-43 Regulates Rab4 Levels to Support Synaptic Vesicle Recycling and Neuromuscular Connectivity in Drosophila and Human ALS Models
2025 M. Gbadamosi, G. Romano, M. Simbula, G. Canarutto, L. Ottoboni, S. Corti, F. Feiguin
C9orf72 Repeat Expansion Induces Metabolic Dysfunction in Human iPSC‐Derived Microglia and Modulates Glial‐Neuronal Crosstalk
2025 M. Mearelli, I. Hirschberg, C. Weissleder, C. Giachino, M.J. Pérez, M. Dubroux, F. Provenzano, M. Rizzuti, L. Ottoboni, U. Sheth, T.F. Gendron, S. Corti, M. Deleidi
Transplanted human striatal progenitors exhibit functional integration and modulate host circuitry in a Huntington’s disease animal model
2025 L. Scaramuzza, M. Ribodino, C. Cassarino, M. Morrocchi, G.B. Gomez Gonzalez, R. Parolisi, E. Sozzi, G. Turrini, V. Cerrato, P. Conforti, E. Hoxha, R. Tognato, G. Galeotti, C. Cordiglieri, M.C. Crosti, S. Zucca, M. Lorenzati, S. Bovetti, P. Spaiardi, C. De'Sperati, G. Biella, L. Ottoboni, M. Parmar, S. Maestri, D. Besusso, E. Cattaneo, A. Buffo
Shaping the Neurovascular Unit Exploiting Human Brain Organoids
2024 M. Rizzuti, V. Melzi, L. Brambilla, L. Quetti, L. Sali, L. Ottoboni, M. Meneri, A. Ratti, F. Verde, N. Ticozzi, G.P. Comi, S. Corti, E. Abati
Unleashing the potential of mRNA therapeutics for inherited neurological diseases
2024 E. Monfrini, G. Baso, D. Ronchi, M. Meneri, D. Gagliardi, L. Quetti, F. Verde, N. Ticozzi, A. Ratti, A. Di Fonzo, G.P. Comi, L. Ottoboni, S. Corti
Improved synthesis and application of an alkyne-functionalized isoprenoid analogue to study the prenylomes of motor neurons, astrocytes and their stem cell progenitors
2024 K.F. Suazo, V. Mishra, S. Maity, S.A. Auger, K. Justyna, A.M. Petre, L. Ottoboni, J. Ongaro, S.P. Corti, F. Lotti, S. Przedborski, M.D. Distefano
Multi-omics profiling of CSF from spinal muscular atrophy type 3 patients after nusinersen treatment: a 2-year follow-up multicenter retrospective study
2023 I. Faravelli, D. Gagliardi, E. Abati, M. Meneri, J. Ongaro, F. Magri, V. Parente, L. Petrozzi, G. Ricci, F. Farè, G. Garrone, M. Fontana, D. Caruso, G. Siciliano, G.P. Comi, A. Govoni, S. Corti, L. Ottoboni
Heparin Precursors with Reduced Anticoagulant Properties Retain Antiviral and Protective Effects That Potentiate the Efficacy of Sofosbuvir against Zika Virus Infection in Human Neural Progenitor Cells
2023 I. Pagani, L. Ottoboni, P. Panina-Bordignon, G. Martino, G. Poli, S. Taylor, J.E. Turnbull, E. Yates, E. Vicenzi
Combined RNA interference and gene replacement therapy targeting MFN2 as proof of principle for the treatment of Charcot-Marie-Tooth type 2A
2023 F. Rizzo, S. Bono, M.D. Ruepp, S. Salani, L. Ottoboni, E. Abati, V. Melzi, C. Cordiglieri, S. Pagliarani, R. De Gioia, A. Anastasia, M. Taiana, M. Garbellini, S. Lodato, P. Kunderfranco, D. Cazzato, D. Cartelli, C. Lonati, N. Bresolin, G. Comi, M. Nizzardo, S. Corti
Identification of Novel Biomarkers of Spinal Muscular Atrophy and Therapeutic Response by Proteomic and Metabolomic Profiling of Human Biological Fluid Samples
2023 M. Meneri, E. Abati, D. Gagliardi, I. Faravelli, V. Parente, A. Ratti, F. Verde, N. Ticozzi, G.P. Comi, L. Ottoboni, S. Corti
iAstrocytes do not restrain T cell proliferation in vitro
2023 E. Colombo, A. De Angelis, C. Bassani, F. Ruffini, L. Ottoboni, L. Garzetti, A. Finardi, G. Martino, R. Furlan, C. Farina
Genomic and transcriptomic advances in amyotrophic lateral sclerosis
2023 M. Rizzuti, L. Sali, V. Melzi, S. Scarcella, G. Costamagna, L. Ottoboni, L. Quetti, L. Brambilla, D. Papadimitriou, F. Verde, A. Ratti, N. Ticozzi, G.P. Comi, S. Corti, D. Gagliardi
Neural stem cell transplantation in patients with progressive multiple sclerosis: an open-label, phase 1 study
2023 A. Genchi, E. Brambilla, F. Sangalli, M. Radaelli, M. Bacigaluppi, R. Furlan, A. Andolfo, D. Drago, C. Magagnotti, G.M. Scotti, R. Greco, P. Vezzulli, L. Ottoboni, M. Bonopane, D. Capilupo, F. Ruffini, D. Belotti, B. Cabiati, S. Cesana, G. Matera, L. Leocani, V. Martinelli, L. Moiola, L. Vago, P. Panina-Bordignon, A. Falini, F. Ciceri, A. Uglietti, M.P. Sormani, G. Comi, M.A. Battaglia, M.A. Rocca, L. Storelli, E. Pagani, G. Gaipa, G. Martino
Targeting PTB for Glia‐to‐Neuron Reprogramming In Vitro and In Vivo for Therapeutic Development in Neurological Diseases
2022 M. Contardo, R. De Gioia, D. Gagliardi, G.P. Comi, L. Ottoboni, M. Nizzardo, S. Corti
Transcriptional effects of fingolimod treatment on peripheral T cells in relapsing remitting multiple sclerosis patients
2022 G. Sferruzza, F. Clarelli, E. Mascia, L. Ferrè, L. Ottoboni, M. Sorosina, S. Santoro, M. Filippi, P. Provero, F. Esposito