CASSANI, BARBARA
CASSANI, BARBARA
Dipartimento di Biotecnologie Mediche e Medicina Traslazionale
Altered intracellular and extracellular signaling leads to impaired T-cell functions in ADA-SCID patients
2008 B. Cassani, M. Mirolo, F. Cattaneo, U. Benninghoff, M. Hershfield, F. Carlucci, A. Tabucchi, C. Bordignon, M. Roncarolo, A. Aiuti
An atypical caspase cascade in adenosine analogs-induced apoptosis of human astrocytoma cells
2002 S. Ceruti, E. Beltrami, B. Cassani, F. Cattabeni, M.P. Abbracchio
Anti-CD3ε mAb improves thymic architecture and prevents autoimmune manifestations in a mouse model of Omenn syndrome : therapeutic implications
2012 V. Marrella, P.L. Poliani, E. Fontana, A. Casati, V. Maina, B. Cassani, F. Ficara, M. Cominelli, F. Schena, M. Paulis, E. Traggiai, P. Vezzoni, F. Grassi, A. Villa
B lymphocytes limit senescence-driven fibrosis resolution and favor hepatocarcinogenesis in mouse liver injury
2018 F. Faggioli, E. Palagano, L. Di Tommaso, M. Donadon, V. Marrella, C. Recordati, S. Mantero, A. Villa, P. Vezzoni, B. Cassani
Bone marrow clonogenic capability, cytokine production, and thymic output in patients with common variable immunodeficiency
2005 A. Isgrò, M. Marziali, I. Mezzaroma, G. Luzi, A. Mazzone, V. Guazzi, G. Andolfi, B. Cassani, A. Aiuti, F. Aiuti
Chromosome Transplantation : Correction of the Chronic Granulomatous Disease Defect in Mouse Induced Pluripotent Stem Cells
2019 A. Castelli, L. Susani, C. Menale, S. Muggeo, E. Caldana, D. Strina, B. Cassani, C. Recordati, E. Scanziani, F. Ficara, A. Villa, P. Vezzoni, M. Paulis
Correction of murine Rag2 severe combined immunodeficiency by lentiviral gene therapy using a codon-optimized RAG2 therapeutic transgene
2012 N. van Til, H. de Boer, N. Mashamba, A. Wabik, M. Huston, T. Visser, E. Fontana, P. Poliani, B. Cassani, F. Zhang, A. Thrasher, A. Villa, G. Wagemaker
Cutaneous barrier leakage and gut inflammation drive skin disease in Omenn syndrome
2020 R. Rigoni, E. Fontana, K. Dobbs, V. Marrella, V. Taverniti, V. Maina, A. Facoetti, G. D'Amico, W. Al-Herz, M.E. Cruz-Munoz, C. Schuetz, A.R. Gennery, E.K. Garabedian, S. Giliani, D. Draper, G. Dbaibo, R.S. Geha, I. Meyts, T. Tousseyn, B. Neven, D. Moshous, A. Fischer, A. Schulz, A. Finocchi, D.B. Kuhns, D.L. Fink, M.S. Lionakis, M. Swamydas, S. Guglielmetti, J. Alejo, I.A. Myles, S. Pittaluga, L.D. Notarangelo, A. Villa, B. Cassani
Defect of regulatory T cells in patients with Omenn syndrome
2010 B. Cassani, L. Poliani, D. Moratto, C. Sobacchi, V. Marrella, L. Imperatori, D. Vairo, A. Plebani, S. Giliani, F. Facchetti, F. Porta, L.D. Notarangelo, A.V.A.R. Badolato
Defective dystrophic thymus determines degenerative changes in skeletal muscle
2021 A. Farini, C. Sitzia, C. Villa, B. Cassani, L. Tripodi, M. Legato, M. Belicchi, P. Bella, C. Lonati, S. Gatti, M. Cerletti, Y. Torrente
Fetal liver cells transplanted in utero rescue the osteopetrotic phenotype in the oc/oc mouse
2009 B. Tondelli, H.C. Blair, M. Guerrini, K.D. Patrene, B. Cassani, P. Vezzoni, F. Lucchini
Gene therapy for primary immunodeficiency
2010 A. Sauer, B. Cassani, A. Aiuti
Homeostatic expansion of autoreactive immunoglobulin secreting cells in the Rag2 mouse model of Omenn Syndrome
2010 B. Cassani, P.L. Poliani, V. Marrella, F. Schena, A.V. Sauer, M. Ravanini, D. Strina, C.E. Busse, S. Regenass, H. Wardemann, A. Martini, F. Facchetti, M. van der Burg, A.G. Rolink, P. Vezzoni, F.M. Grassi, E. Traggiai, A. Villa
Hot spots of retroviral integration in human CD34+ hematopoietic cells
2007 C. Cattoglio, G. Facchini, D. Sartori, A. Antonelli, A. Miccio, B. Cassani, M. Schmidt, C. VON KALLE, S. Howe, A. Thrasher, A. Aiuti, G. Ferrari, A. Recchia, F. Mavilio
Human osteoclast-poor osteopetrosis with hypogammaglobulinemia due to TNFRSF11A (RANK) mutations
2008 M.M. Guerrini, C. Sobacchi, B. Cassani, M. Abinun, S.S. Kilic, A. Pangrazio, D. Moratto, E. Mazzolari, J. Clayton Smith, P. Orchard, F.P. Coxon, M.H. Helfrich, J.C. Crockett, D. Mellis, A. Vellodi, I. Tezcan, L.D. Notarangelo, M.J. Rogers, P. Vezzoni, A. Villa, A. Frattini
Identification of rank mutations in patients with osteoclast-poor autosomal recessive osteopetrosis
2009 M.M. Guerrini, C. Sobacchi, B. Cassani, M. Abinun, S.S. Kilic, A. Pangrazio, D. Moratto, E. Mazzolari, J. Clayton Smith, P. Orchard, F.P. Coxon, M. Helfrich, J. Crockett, L.D. Notarangelo, M. Rogers, P. Vezzoni, A. Frattini, A. Villa
IL-10 critically modulates B cell responsiveness in Rankl-/- mice
2015 V. Marrella, N. Lo Iacono, E. Fontana, C. Sobacchi, H. Sic, F. Schena, L. Sereni, M. Castiello, P. Poliani, P. Vezzoni, B. Cassani, E. Traggiai, A. Villa
Immunoproteasome Inhibition Ameliorates Aged Dystrophic Mouse Muscle Environment
2022 L. Tripodi, D. Molinaro, F.R. Fortunato, C. Mella, B. Cassani, Y. Torrente, A. Farini
In vivo T-cell dynamics during immune reconstitution after hematopoietic stem cell gene therapy in adenosine deaminase severe combined immune deficiency
2011 S. Selleri, I. Brigida, M. Casiraghi, S. Scaramuzza, B. Cappelli, B. Cassani, F. Ferrua, M. Aker, S. Slavin, A. Scarselli, C. Cancrini, S. Marktel, M. Grazia Roncarolo, A. Aiuti
Infantile malignant, autosomal recessive osteopetrosis : the rich and the poor
2009 A. Villa, M.M. Guerrini, B. Cassani, A. Pangrazio, C. Sobacchi