VISCOMI, CARLO FIORE
VISCOMI, CARLO FIORE
Dipartimento di Bioscienze
Model organisms in POLG-related disorders: insights from yeast to multicellular systems
2026 R. Brañas Casas, G. Risato, A. Zuppardo, C. Viscomi, F. Argenton, M. Doimo, N. Facchinello, N. Tiso
Gene therapy for mitochondrial disorders
2024 N. Keshavan, M. Minczuk, C. Viscomi, S. Rahman
Structural rather than catalytic role for mitochondrial respiratory chain supercomplexes
2023 M. Brischigliaro, A. Cabrera-Orefice, S. Arnold, C. Viscomi, M. Zeviani, E. Fernández-Vizarra
Tissue specific requirements for ECSIT in mitochondrial complex i assembly
2023 T.L. Nicol, S. Falcone, A. Blease, P. Vikhe, G. Civiletto, S. Salman, C. Viscomi, K. Patel, P.K. Potter
Mitochondrial Neurodegeneration: Lessons from Drosophila melanogaster Models
2023 M. Brischigliaro, E. Fernandez-Vizarra, C. Viscomi
Mitochondrial DNA Sequencing and Heteroplasmy Quantification by Next Generation Sequencing
2023 A. Legati, D. Ghezzi, C. Viscomi
PPAR-gamma agonist pioglitazone recovers mitochondrial quality control in fibroblasts from PITRM1-deficient patients
2023 A. Di Donfrancesco, C. Berlingieri, M. Giacomello, C. Frascarelli, A.P. Magalhaes Rebelo, L.A. Bindoff, S. Reeval, P. Renbaum, F.M. Santorelli, G. Massaro, C. Viscomi, M. Zeviani, D. Ghezzi, E. Bottani, D. Brunetti
CG7630 is the Drosophila melanogaster homolog of the cytochrome c oxidase subunit COX7B
2022 M. Brischigliaro, A. Cabrera‐orefice, M. Sturlese, D. M Elurbe, E. Frigo, E. Fernandez‐vizarra, S. Moro, M. A Huynen, S. Arnold, C. Viscomi, M. Zeviani
Redox Signaling and Stress in Inherited Myopathies
2022 S. Anil Dogan, G. Giacchin, E. Zito, C. Viscomi
Mitochondrial neurodegeneration
2022 M. Zeviani, C. Viscomi
Role of PITRM1 in Mitochondrial Dysfunction and Neurodegeneration
2021 D. Brunetti, A. Catania, C.F. Viscomi, M. Deleidi, L.A. Bindoff, D. Ghezzi, M. Zeviani
Neural stem cells traffic functional mitochondria via extracellular vesicles to correct mitochondrial dysfunction in target cells
2021 L. Peruzzotti-Jametti, J.D. Bernstock, G. Manferrari, R. Rogall, E. Fernandez-Vizarra, J.C. Williamson, A. Braga, A. Van Den Bosch, T. Leonardi, ?. Kittel, C. Beninc('a), N. Vicario, S. Tan, C. Bastos, I. Bicci, N. Iraci, J.A. Smith, P.J. Lehner, E.I. Buzas, N. Faria, M. Zeviani, C. Frezza, A. Brisson, N.J. Matheson, C. Viscomi, S. Pluchino
DNA polymerase gamma mutations that impair holoenzyme stability cause catalytic subunit depletion
2021 P. Silva-Pinheiro, C. Pardo-Hernandez, A. Reyes, L. Tilokani, A. Mishra, R. Cerutti, S. Li, D.-. Rozsivalova, S. Valenzuela, S.A. Dogan, B. Peter, P. Fernandez-Silva, A. Trifunovic, J. Prudent, M. Minczuk, L. Bindoff, B. Macao, M. Zeviani, M. Falkenberg, C. Viscomi
Structural basis for a complex I mutation that blocks pathological ROS production
2021 Z. Yin, N. Burger, D. Kula-Alwar, D. Aksentijevic, H.R. Bridges, H.A. Prag, D.N. Grba, C. Viscomi, A.M. James, A. Mottahedin, T. Krieg, M.P. Murphy, J. Hirst
Neural stem cells traffic functional mitochondria via extracellular vesicles
2021 L. Peruzzotti-Jametti, J.D. Bernstock, G. Manferrari, R. Rogall, E. Fernandez-Vizarra, J.C. Williamson, A. Braga, A. Van Den Bosch, T. Leonardi, A. Kittel, C. Beninca, N. Vicario, S. Tan, C. Bastos, I. Bicci, N. Iraci, J.A. Smith, P.J. Lehner, E.I. Buzas, N. Faria, M. Zeviani, C. Frezza, A. Brisson, N.J. Matheson, C. Viscomi, S. Pluchino
Exploiting pyocyanin to treat mitochondrial disease due to respiratory complex III dysfunction
2021 R. Peruzzo, S. Corrà, R. Costa, M. Brischigliaro, T. Varanita, L. Biasutto, C. Rampazzo, D. Ghezzi, L. Leanza, M. Zoratti, M. Zeviani, C. De Pittà, C. Viscomi, R. Costa, I. Szabo
Mitochondrial DNA heteroplasmy is modulated during oocyte development propagating mutation transmission
2021 H. Zhang, M. Esposito, M.G. Pezet, J. Aryaman, W. Wei, F. Klimm, C. Calabrese, S.P. Burr, C.H. Macabelli, C. Viscomi, M. Saitou, M.R. Chiaratti, J.B. Stewart, N. Jones, P.F. Chinnery
Respiratory chain signalling is essential for adaptive remodelling following cardiac ischaemia
2020 M. Szibor, R. Schreckenberg, Z. Gizatullina, E. Dufour, M. Wiesnet, P.K. Dhandapani, G. Debska-Vielhaber, J. Heidler, I. Wittig, T.A. Nyman, U. Gartner, A.R. Hall, V. Pell, C. Viscomi, T. Krieg, M.P. Murphy, T. Braun, F.N. Gellerich, K.-. Schluter, H.T. Jacobs
Defective endoplasmic reticulum-mitochondria contacts and bioenergetics in SEPN1-related myopathy
2020 A. Filipe, A. Chernorudskiy, S. Arbogast, E. Varone, R.-. Villar-Quiles, D. Pozzer, M. Moulin, S. Fumagalli, E. Cabet, S. Dudhal, M.-. De Simoni, R. Denis, N. Vadrot, C. Dill, M. Giovarelli, L. Szweda, C. De Palma, P. Pinton, C. Giorgi, C. Viscomi, E. Clementi, S. Missiroli, S. Boncompagni, E. Zito, A. Ferreiro
Strategies for fighting mitochondrial diseases
2020 C. Viscomi, M. Zeviani