IRIS Institutional Research Information System - AIR Archivio Istituzionale della Ricerca

FEDERICI, AUGUSTO BRAMANTE
 Distribuzione geografica
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Continente #
EU - Europa 13.437
NA - Nord America 9.137
AS - Asia 8.866
SA - Sud America 925
AF - Africa 178
OC - Oceania 53
Continente sconosciuto - Info sul continente non disponibili 5
Totale 32.601
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Nazione #
US - Stati Uniti d'America 8.803
GB - Regno Unito 4.036
DE - Germania 3.630
CN - Cina 2.862
SG - Singapore 2.377
IT - Italia 1.542
RU - Federazione Russa 949
SE - Svezia 884
VN - Vietnam 798
BR - Brasile 620
HK - Hong Kong 580
BD - Bangladesh 519
FR - Francia 490
IN - India 453
UA - Ucraina 445
TR - Turchia 380
IE - Irlanda 337
KR - Corea 307
NL - Olanda 288
FI - Finlandia 248
CA - Canada 207
EU - Europa 204
JP - Giappone 158
ID - Indonesia 119
PL - Polonia 111
CO - Colombia 110
AR - Argentina 93
ES - Italia 89
DK - Danimarca 83
GR - Grecia 71
MX - Messico 65
BE - Belgio 51
AU - Australia 42
IQ - Iraq 41
PT - Portogallo 37
CH - Svizzera 35
PH - Filippine 29
ZA - Sudafrica 28
EC - Ecuador 27
AT - Austria 26
PK - Pakistan 25
SA - Arabia Saudita 23
CL - Cile 21
MA - Marocco 21
CI - Costa d'Avorio 20
EG - Egitto 20
TW - Taiwan 20
RO - Romania 17
TN - Tunisia 17
UZ - Uzbekistan 17
AE - Emirati Arabi Uniti 16
IR - Iran 16
MY - Malesia 15
PY - Paraguay 15
VE - Venezuela 15
DZ - Algeria 14
KE - Kenya 14
JO - Giordania 13
IL - Israele 12
PE - Perù 12
KZ - Kazakistan 11
NP - Nepal 11
NZ - Nuova Zelanda 10
RE - Reunion 9
BY - Bielorussia 8
ET - Etiopia 8
HN - Honduras 8
TH - Thailandia 8
UY - Uruguay 8
BG - Bulgaria 7
JM - Giamaica 7
PS - Palestinian Territory 7
AZ - Azerbaigian 6
CR - Costa Rica 6
CZ - Repubblica Ceca 6
HR - Croazia 6
LB - Libano 6
MQ - Martinica 6
OM - Oman 6
PA - Panama 6
BS - Bahamas 5
GE - Georgia 5
QA - Qatar 5
BO - Bolivia 4
EE - Estonia 4
LT - Lituania 4
LU - Lussemburgo 4
RS - Serbia 4
SI - Slovenia 4
SY - Repubblica araba siriana 4
AM - Armenia 3
AO - Angola 3
BB - Barbados 3
GT - Guatemala 3
KW - Kuwait 3
MD - Moldavia 3
MT - Malta 3
MU - Mauritius 3
NI - Nicaragua 3
NO - Norvegia 3
Totale 32.740
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Città #
Southend 3.657
Frankfurt am Main 2.878
Singapore 1.330
Seattle 666
Ashburn 587
San Jose 575
Milan 554
Hong Kong 540
Beijing 531
Chandler 515
Princeton 429
Wilmington 378
Council Bluffs 343
Dublin 332
Jacksonville 327
Santa Clara 320
Dallas 269
Nanjing 257
Redmond 233
Bengaluru 206
Los Angeles 203
Fairfield 194
Ho Chi Minh City 191
Des Moines 190
Mountain View 187
Lauterbourg 177
Sakarya 153
Hanoi 143
Dong Ket 138
Guangzhou 138
Buffalo 136
New York 130
Boardman 128
Moscow 125
Redwood City 125
Woodbridge 125
Houston 121
Ann Arbor 118
Dearborn 116
Andover 99
Somerville 98
Bogotá 93
Serra 92
Shanghai 90
Hanover 89
Jinan 86
Warsaw 86
Shenyang 85
Tianjin 81
Rome 77
Hefei 76
Cambridge 67
São Paulo 65
Jakarta 60
Nanchang 60
Cangzhou 58
Columbus 58
Ottawa 58
Eitensheim 56
Hangzhou 56
The Dalles 55
Tokyo 54
Changsha 51
Toronto 51
Athens 50
Pisa 49
Shenzhen 49
Phoenix 48
Hebei 47
Helsinki 43
Berlin 42
Kunming 36
Roxbury 36
Milwaukee 35
Seoul 35
London 34
San Diego 34
Zhengzhou 34
Bangalore 33
Chicago 31
Jiaxing 29
Madrid 29
Naples 29
Osaka 28
Bitonto 27
Atlanta 26
Brussels 26
Haiphong 25
Istanbul 23
Fuzhou 22
Munich 22
Turin 22
Orem 21
Verona 21
Abidjan 20
Denver 20
Falls Church 20
Mumbai 20
Amsterdam 19
Da Nang 19
Totale 20.670
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Nome #
Type 2B von Willebrand Disease : a Matter of Plasma Plus Platelet Abnormality 703
Diagnosis of inherited von Willebrand disease: a clinical perspective 593
Management of inherited von Willebrand disease in Italy : results from the retrospective study on 1234 patients 538
von Willebrand's disease in the year 2003: towards the complete identification of gene defects for correct diagnosis and treatment 478
A comparison between two semi-quantitative bleeding scales for the diagnosis and assessment of bleeding severity in type 1 von Willebrand disease 323
Bleeding symptoms in patients diagnosed as type 3 Von Willebrand Disease: results from 3WINTERS-IPS, an international and collaborative cross-sectional study 313
National guidelines for dental diagnostic imaging in the developmental age 312
A sensitive ristocetin co-factor activity assay with recombinant glycoprotein Iba for the diagnosis of patients with low von Willebrand factor levels 308
Clinical characteristics and risk factors associated with COVID-19 severity in patients with haematological malignancies in Italy: a retrospective, multicentre, cohort study 300
Gynaecological and obstetrical problems in women with different bleeding disorders 299
Italian daily platelet transfusion practice for haematological patients undergoing high dose chemotherapy with or without stem cell transplantation: a survey by the GIMEMA Haemostasis and Thrombosis Working Party 296
Clinical use of Haemate (R) P in inherited von Willebrand's disease: a cohort study on 100 Italian patients 295
Circulating versus progenitor endothelial cells are abnormal in patients with different types of von willebrand disease and correlate with markers of angiogenesis : a cohort study of 74 cases” 264
Molecular mapping of the chloride binding site in von Willebrand factor (VWF): energetics and conformational effects on the VWF/ADAMTS1-13 254
Markers of angiogenesis in von willbrand disease 252
Identification and characterization of novel variations in platelet G-protein coupled receptor (GPCR) genes in patients historically diagnosed with type 1 von Willebrand disease 248
Expression studies of missense mutations p.D141Y, p.C275S located in the propeptide of von Willebrand factor in patients with type 3 von Willebrand disease 246
Circulating Versus Progenitor Endothelial Cells Levels Are Abnormal in Patients with Different Types of Von Willebrand Disease and Correlate with Markers of Angiogenesis 240
Fifth Åland Island conference on von Willebrand disease 240
Endothelial markers during the desmopressin test in patients with Cushing's syndrome 239
Circulating versus progenitor endothelial cells are abnormal in patients with different types of Von Willebrand disease and correlate with markers of angiogenesis : a cohort study of 74 cases 237
Current challenges in the diagnosis and management of patients with inherited von Willebrand's disease in Italy: An Expert Meeting Report on the diagnosis and surgical and secondary long-term prophylaxis 237
Von Willebrand factor and fibrinolytic parameters during the desmopressin test in patients with Cushing's disease 230
Premature termination codon mutations in the von Willebrand factor gene are associated with allele-specific and position-dependent mRNA decay 227
An intact PDZ motif is essential for correct P2Y12 purinoceptor traffic in human platelets 226
Prevalence of type 2b "Malmo/New York" von Willebrand disease in Italy : the role of von Willebrand factor gene conversion 225
Platelet-dependent von Willebrand factor activity : nomenclature and methodology : communication from the SSC of the ISTH 225
Acquired von Willebrand syndrome associated with hypothyroidism : a mild bleeding disorder to be further investigated 223
Abnormal large platelets are associated not only with von Willebrand Disease (VWD) type 2b but also with severe type 3 : the role of von Willebrand Factor (VWF) defects in the impaired megakaryocytopoiesis 222
Molecular mapping of the chloride binding site in von Willebrand factor (VWF) : energetics and conformational effects on the ADAMTS-13 interaction with wild type and type 2B R1306W VWF forms 219
Activated prothrombin complex concentrate (FEIBA ® ) in acquired haemophilia A: a large multicentre Italian study – the FAIR Registry 217
Impact of therapeutic drug monitoring of antiretroviral drugs in routine clinical management of patients infected with human immunodeficiency virus and related health care costs : a real-life study in a large cohort of patients 216
Genotypes of European and Iranian patients with type 3 von Willebrand disease enrolled in 3WINTERS-IPS 215
Platelet morphological changes in 2 patients with von Willebrand disease type 3 caused by large homozygous deletions of the von Willebrand factor gene 213
BIC International Conference : Abstract Book 211
Pharmacokinetic studies on Wilfactin((R)), a von Willebrand factor concentrate with a low factor VIII content treated with three virus-inactivation/removal methods 210
Unexpected Neurological Symptoms of Ruxolitinib: A Case Report 208
SARS-CoV-2 infection in patients with chronic lymphocytic leukemia: The Italian Hematology Alliance on COVID-19 cohort 206
Phenotype and genotype of a cohort of families historically diagnosed with type 1 von Willebrand disease in the European study, Molecular and Clinical Markers for the Diagnosis and Management of Type 1 von Willebrand Disease (MCMDM-1VWD) 203
Relevance of chloride binding to von Willebrand Factor in type 2b von Willebrand Disease patients 202
Role for platelet von Willebrand factor in supporting platelet-vessel wall interactions in von Willebrand disease 201
Circulating and progenitor endothelial cells are abnormal in patients with different types of von Willebrand disease and correlate with markers of angiogenesis 200
von Willebrand disease in the 21st century: current approaches and new challenges 199
von Willebrand factor in high-purity factor VIII complex concentrates: chaperone protein or key to therapies? : a meeting report 199
Alterata morfologia piastrinica nei pazienti con malattia di von Willebrand tipo 2B e 3 : i dati della microscopia elettronica 199
The von Willebrand Disease type 2a (IIH) : a unique variant of von Willebrand Factor due to combined 2a (IIc)/2n defects 193
Mutations leading to premature termination codons in the Von Willebrand factor gene are associated with the decay of the mutant mRNAs 190
Molecular mapping of chloride binding site in VWF : energetics and conformational effects on the VWF/ADAMTS-13 interaction 190
Third Åland islands conference on von Willebrand disease, 26-28 September 2012 : meeting report 190
Update on the management of von Willebrand disease 189
Prophylaxis of bleeding episodes in patients with von Willebrand's disease 189
Relevance of chloride binding to von Willebrand factor in type 2B von Willebrand disease patients 188
Validation of a rapid test (VWF-LIA) for the quantitative determination of von Willebrand factor antigen in type 1 von Willebrand disease diagnosis within the European multicenter study MCMDM-1VWD 188
Contemporary issues in the management of von Willebrand disease 188
Supportive transfusion therapy in cancer patients with acquired defects of hemostasis 185
State of the art : von Willebrand disease 183
Prophylaxis in severe forms of von Willebrand's disease : results from the von Willebrand Disease Prophylaxis Network, (VWD PN) 182
Detailed von Willebrand factor multimer analysis in patients with von Willebrand disease in the European study, molecular and clinical markers for the diagnosis and management of type 1 von Willebrand disease (MCMDM-1VWD : reply to a rebuttal 179
A new candidate mutation, G1629R, in a patient with type 2A von Willebrand's disease: basic mechanisms and clinical implications 178
Evaluation of a new turbidimetric assay for von Willebrand factor activity useful in the general screening of von Willebrand disease 177
The natural history of hepatitis C virus infection in Italian patients with von Willebrand's disease : A cohort study 176
Abnormal VWF modifies megakaryocytopoiesis : studies of platelets and megakaryocyte cultures from patients with von Willebrand disease type 2B 176
Understanding FVIII/VWF complex : report from a symposium of XXIX WFH meeting 2010 176
Use of intravenous immunoglobulin in patients with acquired von Willebrand syndrome 175
The use of desmopressin in von Willebrand disease: the experience of the first 30 years (1977–2007) 175
Changes in bleeding patterns in von Willebrand disease after institution of long-term replacement therapy : results from the von Willebrand Disease Prophylaxis Network 175
Successful loco-regional thrombolytic treatment of the aortic conduit in a patient with orthotopic liver transplantation: a case report 174
Type 2A (IIH) von Willebrand disease is due to mutations that affect von Willebrand factor multimerization 174
First report of reproductive assistance in a woman affected by May-Hegglin anomaly 174
Current and emerging approaches for assessing von Willebrand disease in 2016 174
Prophylaxis in patients with von Willebrand disease : who, when, how? 173
Evaluation and management of postpartum hemorrhage : consensus from an international expert panel 171
HDL/ApoA-I : role in VWF-dependent thrombosis 169
Diagnosis and management of inherited von Willebrand disease in the next decade : panel discussion 168
The natural history of occult or angiodysplastic gastrointestinal bleeding in von Willebrand disease 168
Towards a more automatic and rapid laboratory diagnosis of von Willebrand disease 168
Biochemical characterization of a recombinant von Willebrand factor (VWF) with combined type 2B and type 1 defects in the VWF gene in two patients with a type 2A phenotype of von Willebrand disease 167
Elevation of von Willebrand factor is independent of erythrocyte sedimentation rate and persists after glucocorticoid treatment in giant cell arteritis 167
Sialic acid prevents loss of large von Willebrand factor multimers by protecting against amino-terminal proteolytic cleavage 167
The 80th anniversary of von Willebrand's disease: history, management and research 165
A type 2b von Willebrand disease mutation (Ile546-->Val) associated with an unusual phenotype 163
An association of candidate gene haplotypes and bleeding severity in von Willebrand disease type 2A, 2B, and 2M pedigrees 163
Naturally occurring anticoagulants and bone marrow transplantation: plasma protein C predicts the development of venocclusive disease of the liver 163
Identification of type 1 von Willebrand disease patients with reduced von Willebrand factor survival by assay of the VWF propeptide in the European study: molecular and clinical markers for the diagnosis and management of type 1 VWD (MCMDM-1VWD) 163
Heterogeneity of type I von Willebrand disease : evidence for a subgroup with an abnormal von Willebrand factor 162
Transfusion issues in cancer patients 162
von Willebrand disease type 2B must be always considered in the differential diagnosis of genetic thrombocytopenias with giant platelets 161
The natural VWF mutant P.R1306W, causing a type 2B VWD, binds, chloride ions with lower affinity than WT VWD and is cleaved more efficently by ADAMTS-13 161
Von Willebrand factor promotes endothelial cell adhesion via an Arg-Gly-Asp-dependent mechanism 161
Von Willebrand factor variant p.Arg924Gln marks an allele associated with reduced von Willebrand factor and factor VIII levels 160
Adhesive properties of the carbohydrate-modified von Willebrand factor (CHO-vWF) 160
Efficacy and safety during formulation switch of a pasteurized VWF/FVIII concentrate : results from an Italian prospective observational study in patients with von Willebrand disease 160
Treatment of acquired von Willebrand syndrome in childhood 160
von Willebrand disease and other bleeding disorders in women : consensus on diagnosis and management from an international expert panel 159
Activation-independent platelet adhesion and aggregation under elevated shear stress 157
Mutations leading to premature termination codons in the Von Willebrand factor gene are associated with allele-specific mRNAs decay 157
The impact of bleeding history, von Willebrand factor and PFA-100(®) on the diagnosis of type 1 von Willebrand disease : results from the European study MCMDM-1VWD 157
Type 2B “Malmo or New York” is not so rare among Italian patients with von Willebrand disease : the role of P1266l/Q mutations of the von Willebrand factor gene in eight cases 156
Epidemiology and general guidelines of the management of acquired haemophilia and von Willebrand syndrome 154
A quantitative analysis of bleeding symptoms in type 1 von Willebrand disease : results from a multicenter European study (MCMDM-1 VWD) 154
Totale 21.525
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Categoria #
all - tutte 83.020
article - articoli 0
book - libri 0
conference - conferenze 0
curatela - curatele 0
other - altro 0
patent - brevetti 0
selected - selezionate 0
volume - volumi 0
Totale 83.020
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Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2020/2021221 0 0 0 0 0 0 0 0 0 0 0 221
2021/20222.064 195 92 45 81 173 149 208 130 138 225 140 488
2022/20232.371 328 181 196 245 315 506 36 118 247 39 97 63
2023/20243.169 68 132 61 53 235 109 419 386 213 432 500 561
2024/20254.430 490 674 363 421 282 140 99 456 228 247 361 669
2025/20268.657 781 507 1.022 564 728 599 840 543 924 570 772 807
Totale 34.442