IRIS Institutional Research Information System - AIR Archivio Istituzionale della Ricerca

FEDERICI, AUGUSTO BRAMANTE
 Distribuzione geografica
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Continente #
EU - Europa 12.036
NA - Nord America 6.374
AS - Asia 3.999
SA - Sud America 343
AF - Africa 48
OC - Oceania 45
Continente sconosciuto - Info sul continente non disponibili 3
Totale 22.848
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Nazione #
US - Stati Uniti d'America 6.203
GB - Regno Unito 3.944
DE - Germania 3.555
CN - Cina 1.600
IT - Italia 1.084
SE - Svezia 872
SG - Singapore 862
RU - Federazione Russa 597
UA - Ucraina 434
TR - Turchia 362
IE - Irlanda 332
IN - India 318
FR - Francia 278
KR - Corea 278
NL - Olanda 252
FI - Finlandia 217
VN - Vietnam 211
EU - Europa 204
BR - Brasile 186
CA - Canada 137
JP - Giappone 106
ID - Indonesia 98
CO - Colombia 91
PL - Polonia 86
DK - Danimarca 80
GR - Grecia 65
ES - Italia 58
BE - Belgio 48
HK - Hong Kong 36
AU - Australia 35
AR - Argentina 31
CH - Svizzera 29
PT - Portogallo 27
MX - Messico 20
PH - Filippine 18
TW - Taiwan 18
AT - Austria 16
RO - Romania 15
CL - Cile 11
EC - Ecuador 10
NZ - Nuova Zelanda 10
AE - Emirati Arabi Uniti 9
DZ - Algeria 9
IR - Iran 9
MY - Malesia 9
PK - Pakistan 9
RE - Reunion 9
IL - Israele 8
BG - Bulgaria 6
CZ - Repubblica Ceca 6
EG - Egitto 6
HR - Croazia 6
MA - Marocco 5
MQ - Martinica 5
OM - Oman 5
SA - Arabia Saudita 5
TN - Tunisia 5
VE - Venezuela 5
BY - Bielorussia 4
EE - Estonia 4
PE - Perù 4
SI - Slovenia 4
UZ - Uzbekistan 4
ZA - Sudafrica 4
BD - Bangladesh 3
GE - Georgia 3
HN - Honduras 3
IQ - Iraq 3
JO - Giordania 3
KZ - Kazakistan 3
LT - Lituania 3
RS - Serbia 3
AM - Armenia 2
AZ - Azerbaigian 2
HU - Ungheria 2
KE - Kenya 2
KH - Cambogia 2
MD - Moldavia 2
MR - Mauritania 2
MT - Malta 2
MU - Mauritius 2
NO - Norvegia 2
NP - Nepal 2
PA - Panama 2
PS - Palestinian Territory 2
PY - Paraguay 2
SD - Sudan 2
SK - Slovacchia (Repubblica Slovacca) 2
SY - Repubblica araba siriana 2
UY - Uruguay 2
AN - Antille olandesi 1
BN - Brunei Darussalam 1
BO - Bolivia 1
CU - Cuba 1
CY - Cipro 1
LA - Repubblica Popolare Democratica del Laos 1
LB - Libano 1
LK - Sri Lanka 1
LV - Lettonia 1
NG - Nigeria 1
Totale 23.044
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Città #
Southend 3.657
Frankfurt am Main 2.840
Seattle 650
Chandler 515
Singapore 509
Milan 485
Princeton 429
Beijing 382
Wilmington 377
Dublin 327
Jacksonville 326
Council Bluffs 281
Nanjing 249
Redmond 230
Ashburn 209
Fairfield 194
Mountain View 187
Des Moines 186
Santa Clara 172
Sakarya 153
Dong Ket 138
Bengaluru 133
Redwood City 125
Woodbridge 125
Ann Arbor 116
Dearborn 116
Houston 114
Boardman 109
Andover 99
Somerville 98
Serra 92
Hanover 89
Bogotá 85
Jinan 83
Shenyang 83
Warsaw 75
Cambridge 66
Nanchang 59
Shanghai 57
Eitensheim 56
Guangzhou 56
Jakarta 54
Ottawa 54
Athens 49
Hebei 47
Pisa 46
Changsha 45
Tianjin 43
Toronto 42
Berlin 39
Hangzhou 36
Kunming 36
Roxbury 36
Phoenix 35
Bangalore 33
San Diego 33
Milwaukee 29
Zhengzhou 29
Jiaxing 28
Bitonto 27
Brussels 25
Los Angeles 24
Rome 24
Osaka 23
London 22
Fuzhou 21
Helsinki 21
Falls Church 20
São Paulo 20
Hamburg 19
Istanbul 19
Madrid 19
New York 19
Chicago 18
Duncan 18
Hong Kong 17
Taipei 17
Auburn Hills 16
Verona 16
Haikou 15
Silver Spring 15
Buenos Aires 14
Bühl 14
Edinburgh 14
Hefei 14
Ningbo 14
Wuhan 14
Saint Petersburg 13
Taizhou 13
Tokyo 13
Atlanta 12
Chesterfield 12
Fremont 12
Kiselëv 12
Amsterdam 11
Chengdu 11
Lanzhou 11
Nuremberg 11
Seoul 11
Yubileyny 11
Totale 15.718
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Nome #
Type 2B von Willebrand Disease : a Matter of Plasma Plus Platelet Abnormality 526
Diagnosis of inherited von Willebrand disease: a clinical perspective 488
Management of inherited von Willebrand disease in Italy : results from the retrospective study on 1234 patients 371
von Willebrand's disease in the year 2003: towards the complete identification of gene defects for correct diagnosis and treatment 357
Clinical use of Haemate (R) P in inherited von Willebrand's disease: a cohort study on 100 Italian patients 230
Gynaecological and obstetrical problems in women with different bleeding disorders 216
Circulating versus progenitor endothelial cells are abnormal in patients with different types of von willebrand disease and correlate with markers of angiogenesis : a cohort study of 74 cases” 216
Italian daily platelet transfusion practice for haematological patients undergoing high dose chemotherapy with or without stem cell transplantation: a survey by the GIMEMA Haemostasis and Thrombosis Working Party 207
Bleeding symptoms in patients diagnosed as type 3 Von Willebrand Disease: results from 3WINTERS-IPS, an international and collaborative cross-sectional study 204
Clinical characteristics and risk factors associated with COVID-19 severity in patients with haematological malignancies in Italy: a retrospective, multicentre, cohort study 201
Endothelial markers during the desmopressin test in patients with Cushing's syndrome 195
Circulating Versus Progenitor Endothelial Cells Levels Are Abnormal in Patients with Different Types of Von Willebrand Disease and Correlate with Markers of Angiogenesis 192
Premature termination codon mutations in the von Willebrand factor gene are associated with allele-specific and position-dependent mRNA decay 191
Expression studies of missense mutations p.D141Y, p.C275S located in the propeptide of von Willebrand factor in patients with type 3 von Willebrand disease 188
Markers of angiogenesis in von willbrand disease 187
Acquired von Willebrand syndrome associated with hypothyroidism : a mild bleeding disorder to be further investigated 186
Identification and characterization of novel variations in platelet G-protein coupled receptor (GPCR) genes in patients historically diagnosed with type 1 von Willebrand disease 185
National guidelines for dental diagnostic imaging in the developmental age 184
A sensitive ristocetin co-factor activity assay with recombinant glycoprotein Iba for the diagnosis of patients with low von Willebrand factor levels 183
An intact PDZ motif is essential for correct P2Y12 purinoceptor traffic in human platelets 180
Circulating versus progenitor endothelial cells are abnormal in patients with different types of Von Willebrand disease and correlate with markers of angiogenesis : a cohort study of 74 cases 179
Abnormal large platelets are associated not only with von Willebrand Disease (VWD) type 2b but also with severe type 3 : the role of von Willebrand Factor (VWF) defects in the impaired megakaryocytopoiesis 177
Role for platelet von Willebrand factor in supporting platelet-vessel wall interactions in von Willebrand disease 170
Platelet morphological changes in 2 patients with von Willebrand disease type 3 caused by large homozygous deletions of the von Willebrand factor gene 169
Update on the management of von Willebrand disease 166
von Willebrand factor in high-purity factor VIII complex concentrates: chaperone protein or key to therapies? : a meeting report 165
Prevalence of type 2b "Malmo/New York" von Willebrand disease in Italy : the role of von Willebrand factor gene conversion 164
The von Willebrand Disease type 2a (IIH) : a unique variant of von Willebrand Factor due to combined 2a (IIc)/2n defects 161
Von Willebrand factor and fibrinolytic parameters during the desmopressin test in patients with Cushing's disease 161
Fifth Åland Island conference on von Willebrand disease 161
Molecular mapping of the chloride binding site in von Willebrand factor (VWF): energetics and conformational effects on the VWF/ADAMTS1-13 160
Alterata morfologia piastrinica nei pazienti con malattia di von Willebrand tipo 2B e 3 : i dati della microscopia elettronica 159
Third Åland islands conference on von Willebrand disease, 26-28 September 2012 : meeting report 158
Mutations leading to premature termination codons in the Von Willebrand factor gene are associated with the decay of the mutant mRNAs 156
Prophylaxis of bleeding episodes in patients with von Willebrand's disease 154
Activated prothrombin complex concentrate (FEIBA ® ) in acquired haemophilia A: a large multicentre Italian study – the FAIR Registry 154
Detailed von Willebrand factor multimer analysis in patients with von Willebrand disease in the European study, molecular and clinical markers for the diagnosis and management of type 1 von Willebrand disease (MCMDM-1VWD : reply to a rebuttal 153
Supportive transfusion therapy in cancer patients with acquired defects of hemostasis 153
von Willebrand disease in the 21st century: current approaches and new challenges 151
Impact of therapeutic drug monitoring of antiretroviral drugs in routine clinical management of patients infected with human immunodeficiency virus and related health care costs : a real-life study in a large cohort of patients 151
Relevance of chloride binding to von Willebrand Factor in type 2b von Willebrand Disease patients 149
BIC International Conference : Abstract Book 149
Current challenges in the diagnosis and management of patients with inherited von Willebrand's disease in Italy: An Expert Meeting Report on the diagnosis and surgical and secondary long-term prophylaxis 148
Molecular mapping of the chloride binding site in von Willebrand factor (VWF) : energetics and conformational effects on the ADAMTS-13 interaction with wild type and type 2B R1306W VWF forms 146
Prophylaxis in severe forms of von Willebrand's disease : results from the von Willebrand Disease Prophylaxis Network, (VWD PN) 143
Validation of a rapid test (VWF-LIA) for the quantitative determination of von Willebrand factor antigen in type 1 von Willebrand disease diagnosis within the European multicenter study MCMDM-1VWD 142
Sialic acid prevents loss of large von Willebrand factor multimers by protecting against amino-terminal proteolytic cleavage 142
Molecular mapping of chloride binding site in VWF : energetics and conformational effects on the VWF/ADAMTS-13 interaction 141
Successful loco-regional thrombolytic treatment of the aortic conduit in a patient with orthotopic liver transplantation: a case report 139
Pharmacokinetic studies on Wilfactin((R)), a von Willebrand factor concentrate with a low factor VIII content treated with three virus-inactivation/removal methods 138
Phenotype and genotype of a cohort of families historically diagnosed with type 1 von Willebrand disease in the European study, Molecular and Clinical Markers for the Diagnosis and Management of Type 1 von Willebrand Disease (MCMDM-1VWD) 138
Contemporary issues in the management of von Willebrand disease 138
The natural history of hepatitis C virus infection in Italian patients with von Willebrand's disease : A cohort study 137
Platelet-dependent von Willebrand factor activity : nomenclature and methodology : communication from the SSC of the ISTH 137
Relevance of chloride binding to von Willebrand factor in type 2B von Willebrand disease patients 136
Abnormal VWF modifies megakaryocytopoiesis : studies of platelets and megakaryocyte cultures from patients with von Willebrand disease type 2B 136
Evaluation of a new turbidimetric assay for von Willebrand factor activity useful in the general screening of von Willebrand disease 135
An association of candidate gene haplotypes and bleeding severity in von Willebrand disease type 2A, 2B, and 2M pedigrees 134
Unexpected Neurological Symptoms of Ruxolitinib: A Case Report 133
Treatment of acquired von Willebrand syndrome in childhood 132
Diagnosis and management of inherited von Willebrand disease in the next decade : panel discussion 130
Type 2A (IIH) von Willebrand disease is due to mutations that affect von Willebrand factor multimerization 129
Circulating and progenitor endothelial cells are abnormal in patients with different types of von Willebrand disease and correlate with markers of angiogenesis 129
State of the art : von Willebrand disease 129
Mutations leading to premature termination codons in the Von Willebrand factor gene are associated with allele-specific mRNAs decay 128
The natural history of occult or angiodysplastic gastrointestinal bleeding in von Willebrand disease 128
The impact of bleeding history, von Willebrand factor and PFA-100(®) on the diagnosis of type 1 von Willebrand disease : results from the European study MCMDM-1VWD 127
Naturally occurring anticoagulants and bone marrow transplantation: plasma protein C predicts the development of venocclusive disease of the liver 126
Towards a more automatic and rapid laboratory diagnosis of von Willebrand disease 126
Von Willebrand factor promotes endothelial cell adhesion via an Arg-Gly-Asp-dependent mechanism 125
First report of reproductive assistance in a woman affected by May-Hegglin anomaly 124
Identification of type 1 von Willebrand disease patients with reduced von Willebrand factor survival by assay of the VWF propeptide in the European study: molecular and clinical markers for the diagnosis and management of type 1 VWD (MCMDM-1VWD) 124
Genotypes of European and Iranian patients with type 3 von Willebrand disease enrolled in 3WINTERS-IPS 124
Epidemiology and general guidelines of the management of acquired haemophilia and von Willebrand syndrome 123
A type 2b von Willebrand disease mutation (Ile546-->Val) associated with an unusual phenotype 123
Detailed von Willebrand factor multimer analysis in patients with von Willebrand disease in the European study, molecular and clinical markers for the diagnosis and management of type 1 von Willebrand disease (MCMDM-1VWD) 123
Multimeric composition of factor VIII/von Willebrand factor following administration of DDAVP : implications for pathophysiology and therapy of von Willebrand's disease subtypes 123
Efficacy and safety during formulation switch of a pasteurized VWF/FVIII concentrate : results from an Italian prospective observational study in patients with von Willebrand disease 123
A new variant of type II von Willebrand disease with aberrant multimeric structure of plasma but not platelet von Willebrand factor (type IIF) 123
Use of intravenous immunoglobulin in patients with acquired von Willebrand syndrome 121
The natural VWF mutant P.R1306W, causing a type 2B VWD, binds, chloride ions with lower affinity than WT VWD and is cleaved more efficently by ADAMTS-13 121
Prophylaxis in patients with von Willebrand disease : who, when, how? 121
Type 2B “Malmo or New York” is not so rare among Italian patients with von Willebrand disease : the role of P1266l/Q mutations of the von Willebrand factor gene in eight cases 120
Changes in bleeding patterns in von Willebrand disease after institution of long-term replacement therapy : results from the von Willebrand Disease Prophylaxis Network 119
The 80th anniversary of von Willebrand's disease: history, management and research 118
Acquired von Willebrand syndrome type 2A in a JAK2-positive essential thrombocythaemia-affected member of a large von Willebrand disease family with a novel autosomal dominant A1716P mutation 118
Elevation of von Willebrand factor is independent of erythrocyte sedimentation rate and persists after glucocorticoid treatment in giant cell arteritis 118
Activation-independent platelet adhesion and aggregation under elevated shear stress 117
von Willebrand disease and other bleeding disorders in women : consensus on diagnosis and management from an international expert panel 117
Carbohydrate moiety of von Willebrand factor is not necessary for maintaining multimeric structure and ristocetin cofactor activity but protects from proteolytic degradation 117
A new candidate mutation, G1629R, in a patient with type 2A von Willebrand's disease: basic mechanisms and clinical implications 117
Transfusion issues in cancer patients 114
Current and emerging approaches for assessing von Willebrand disease in 2016 114
Molecular characterization of a multiethnic group of 21 patients with type 3 von Willebrand disease 113
Linkage analysis in families diagnosed with type 1 von Willebrand disease in the European study, molecular and clinical markers for the diagnosis and management of type 1 VWD 112
von Willebrand factor collagen binding assay in von Willebrand disease type 2A, 2B, and 2M 112
von Willebrand factor synthesized by endothelial cells from a patient with type IIB von Willebrand disease supports platelet adhesion normally but has an increased affinity for platelets 112
Multiple dental extractions with a new prothrombin complex concentrate in two patients with factor VIII inhibitors 112
von Willebrand disease type 2B must be always considered in the differential diagnosis of genetic thrombocytopenias with giant platelets 111
A quantitative analysis of bleeding symptoms in type 1 von Willebrand disease : results from a multicenter European study (MCMDM-1 VWD) 111
Totale 15.724
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Categoria #
all - tutte 58.512
article - articoli 0
book - libri 0
conference - conferenze 0
curatela - curatele 0
other - altro 0
patent - brevetti 0
selected - selezionate 0
volume - volumi 0
Totale 58.512
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Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2019/2020506 0 0 0 0 0 0 0 0 0 300 137 69
2020/20212.466 72 235 216 36 246 138 127 115 323 110 627 221
2021/20222.064 195 92 45 81 173 149 208 130 138 225 140 488
2022/20232.371 328 181 196 245 315 506 36 118 247 39 97 63
2023/20243.169 68 132 61 53 235 109 419 386 213 432 500 561
2024/20253.156 490 674 363 421 282 140 99 456 228 3 0 0
Totale 24.511