Management of systemic mastocytosis is an emerging challenge which requires a multidisciplinary diagnostic approach and personalized treatment strategy. Midostaurin can rapidly reduce the disease burden, also in cladribine refractory cases.

A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin / M. Sciume, F. Serpenti, S. Muratori, V. Pravettoni, F.M. Ulivieri, G.A. Croci, A.C. Migliorini, A. Esposito, M.C. Goldaniga, G.N. Saporiti, G. Galassi, L. Baldini, F. Onida, F.I. Grifoni. - In: CLINICAL CASE REPORTS. - ISSN 2050-0904. - 9:2(2021 Feb), pp. 978-982. [10.1002/ccr3.3717]

A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin

F. Serpenti
Secondo
;
G.A. Croci;A. Esposito;G.N. Saporiti;L. Baldini;F. Onida
Penultimo
;
2021

Abstract

Management of systemic mastocytosis is an emerging challenge which requires a multidisciplinary diagnostic approach and personalized treatment strategy. Midostaurin can rapidly reduce the disease burden, also in cladribine refractory cases.
bulky lymphadenopathy; midostaurin; purine analogue; systemic mastocytosis;
Settore MED/08 - Anatomia Patologica
feb-2021
29-dic-2020
Article (author)
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/2434/905921
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