TEDESCO, BARBARA
TEDESCO, BARBARA
Dipartimento di Scienze Farmacologiche e Biomolecolari
A Crucial Role for the Protein Quality Control System in Motor Neuron Diseases
2020 R. Cristofani, V. Crippa, M.E. Cicardi, B. Tedesco, V. Ferrari, M. Chierichetti, E. Casarotto, M. Piccolella, E. Messi, M. Galbiati, P. Rusmini, A. Poletti
Aberrant biochemical and functional behaviour of P209 mutants of the Bcl-2-Associated Athanogene 3
2019 B. Tedesco, E. Adriaenssens, L. Mediani, V. Crippa, S. Carra, V. Timmerman, A. Poletti
ALS-associeted VCP-mutants lead to lysosome damage
2019 V. Ferrari, M.E. Cicardi, P. Rusmini, V. Crippa, R. Cristofani, B. Tedesco, M. Galbiati, E. Messi, M. Piccolella, A. Poletti
Alternative translation initiatin as a novel strategy to block toxicity of the mutant androgen receptor in SBMA
2019 R. Cristofani, P. Rusmini, M. Galbiati, V. Crippa, M. Chierichetti, V. Ferrari, B. Tedesco, E. Casarotto, M. Pennuto, A. Poletti
Alternative Translation Initiation as a novel strategy to block toxicity of the mutant Androgen Receptor in SBMA
2023 M. Chierichetti, R. Cristofani, P. Rusmini, V. Ferrari, B. Tedesco, M. Cozzi, E. Casarotto, F. Mina, P. Pramaggiore, V. Crippa, M. Galbiati, M. Piccolella, A. Poletti
Analysis of the autophagic response in models of KIF5A-related neurodegeneration
2021 M. Cozzi, B. Tedesco, R. Cristofani, M. Galbiati, P. Rusmini, V. Crippa, M. Piccolella, V. Ferrari, E. Casarotto, M. Chierichetti, F. Mina, C. Gellera, S. Magri, F. Taroni, A. Poletti
Analysis of the pathogenetic mechanisms involved in KIF5A-related neurodegenerative disorders
2022 M. Cozzi, B. Tedesco, R.M. Cristofani, V. Ferrari, E. Casarotto, M. Chierichetti, F. Mina, G. Avella, M. Piccolella, M. Galbiati, P. Rusmini, V. Crippa, C. Gellera, S. Magri, S. Santangelo, A. Ratti, F. Taroni, A. Poletti
Androgen receptor with an elongated polyglutamine tract dysregulates muscle expression of myo-miRs and of their target genes.
2021 M. Galbiati, P. Rusmini, V. Crippa, R.M. Cristofani, V. Ferrari, B. Tedesco, E. Casarotto, M. Chierichetti, M. Cozzi, F. Mina, S. Fenu, D. Pareyson, C. Malacarne, S. Bonanno, S. Marcuzzo, A. Poletti
Autophagic and Proteasomal Mediated Removal of Mutant Androgen Receptor in Muscle Models of Spinal and Bulbar Muscular Atrophy
2019 M.E. Cicardi, R. Cristofani, V. Crippa, V. Ferrari, B. Tedesco, E. Casarotto, M. Chierichetti, M. Galbiati, M. Piccolella, E. Messi, S. Carra, M. Pennuto, P. Rusmini, A. Poletti
Autophagy mediated HSPB8 removal of aggregating dipeptides produced in C9ORF72 related neurodegenerative diseases
2017 R. Cristofani, G. Vezzoli, P. Rusmini, M. Galbiati, M.E. Cicardi, M. Meroni, V. Ferrari, B. Tedesco, V. Crippa, A. Poletti
BAG1 assists the degradation of neurotoxic proteins related to motor neuron diseases counteracting dynein-mediated autophagy alteration
2021 R. Cristofani, M. Cozzi, B. Tedesco, V. Ferrari, E. Casarotto, M. Chierichetti, M. Galbiati, P. Rusmini, V. Crippa, A. Poletti
BAG3 Pro209 mutants associated with myopathy and neuropathy relocate chaperones of the CASA-complex to aggresomes
2020 E. Adriaenssens, B. Tedesco, L. Mediani, B. Asselbergh, V. Crippa, F. Antoniani, S. Carra, A. Poletti, V. Timmerman
Bcl2-Associated Athanogene 3 mutants : solubility and aggregation prone behaviour assessment by different techniques
2019 B. Tedesco, E. Adriaenssens, L. Mediani, V. Crippa, S. Carra, V. Timmerman, A. Poletti
Bicalutamide and Trehalose Ameliorate Spinal and Bulbar Muscular Atrophy Pathology in Mice
2023 M. Galbiati, M. Meroni, M. Boido, M. Cescon, P. Rusmini, V. Crippa, R. Cristofani, M. Piccolella, V. Ferrari, B. Tedesco, E. Casarotto, M. Chierichetti, M. Cozzi, F. Mina, M.E. Cicardi, S. Pedretti, N. Mitro, A. Caretto, P. Risè, A. Sala, A.P. Lieberman, P. Bonaldo, M. Pennuto, A. Vercelli, A. Poletti
Bicalutamide and Trehalose as a therapeutic approach for SBMA
2023 M. Galbiati, P. Rusmini, V. Crippa, M. Cescon, R. Cristofani, V. Ferrari, E. Casarotto, B. Tedesco, M. Chierichetti, M. Cozzi, M. Boido, A. Poletti
C9ORF72 arginine rich poly-dipeptides induce transcriptional alterations in ALS/FTD cell model
2019 R.M. Cristofani, A. Grilli, G. Vezzoli, N. Valentina Licata, V. Crippa, M.E. Cicardi, P. Rusmini, B. Tedesco, V. Ferrari, E. Casarotto, M. Chierichetti, M. Galbiati, S. Carra, S. Bicciato, A. Provenzani, A. Poletti
Chaperone Assisted Selective Autophagy (CASA) a potential target for therapeutics in motoneuron diseases
2018 V. Crippa, P. Rusmini, R. Cristofani, M.E. Cicardi, M. Meroni, V. Ferrari, B. Tedesco, M. Piccolella, E. Messi, M. Galbiati, A. Poletti
Chaperone mediated autophagy respond to dynein mediated transport inhibition in motor neuron diseases
2018 R.M. Cristofani, V. Crippa, M.E. Cicardi, P. Rusmini, M. Meroni, V. Ferrari, B. Tedesco, M. Galbiati, S. Gessica, F. Carlo, A. Poletti
Chaperone mediated autophagy responds to macroautophagy inhibition in motor neuron diseases
2018 R.M. Cristofani, V. Crippa, M.E. Cicardi, P. Rusmini, M. Meroni, V. Ferrari, B. Tedesco, M. Galbiati, E. Messi, M. Piccolella, G. Sala, C. Ferrarese, A. Poletti
Characterization of two new mutations in the small Heat Shock protein B8 HSPB8 and impact in Amyotrophic Lateral Sclerosis cell models
2018 B. Tedesco, V. Crippa, P. Rusmini, R. Cristofani, M.E. Cicardi, V. Ferrari, G. Vezzoli, M. Meroni, E. Messi, M. Piccolella, R. Galbiati, A. Poletti