TEDESCO, BARBARA

TEDESCO, BARBARA  

Dipartimento di Scienze Farmacologiche e Biomolecolari Rodolfo Paoletti  

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Titolo Data di pubblicazione Autori Tipo File Abstract
Aberrant interplay between the mutant androgen receptor and GLI3: highlighting a potential neurodevelopmental weakness in Kennedy’s Disease 2026 Marta CozziMaria Elena CicardiLaura CornaggiaPaola PramaggioreBarbara TedescoVeronica FerrariMarta ChierichettiAli MohamedVeronica MarchesiAnnalisa BrivioMargherita PiccolellaMariarita GalbiatiPaola RusminiValeria CrippaRiccardo CristofaniAngelo Poletti + Conference Object -
MUSCLE MITOCHONDRIAL DYSFUNCTIONS AND SYSTEMIC LIPIDOMIC REMODELING IN SBMA 2026 Ali MohamedRiccardo CristofaniMarta CozziVeronica FerrariMarta ChierichettiBarbara TedescoElsa FranchiMarco BusnelliGiulia ChiesaValeria CrippaPaola RusminiAngelo PolettiMariarita Galbiati + Conference Object -
Molecular, cellular, and clinical aspects of myofibrillar myopathy caused by HSPB8 frameshift mutations 2026 Marchesi, VeronicaPoletti, AngeloTedesco, Barbara + Article (author) -
FAK signaling pathways are modulated by HSPB8 and BAG3 in breast cancer 2026 Piccolella, MargheritaTedesco, BarbaraFerrari, VeronicaFilippone, Maria GraziaTucci, Francesco AntonioCasarotto, ElenaCozzi, MartaChierichetti, MartaPramaggiore, PaolaCornaggia, LauraMagdalena, RocioMohamed, AliBrodnanova, MariaKoshal, PrashantRusmini, PaolaGalbiati, MariaritaTosoni, DanielaPece, SalvatoreCristofani, RiccardoCrippa, ValeriaPoletti, Angelo + Article (author) -
The alternative androgen receptor isoform a mitigates toxicity of polyglutamine-elongated mutant androgen receptor in spinal and bulbar muscular atrophy 2026 Chierichetti, MartaTedesco, BarbaraFerrari, VeronicaCornaggia, LauraPramaggiore, PaolaCozzi, MartaMohamed, AliMagdalena, RocioPiccolella, MargheritaCrippa, ValeriaRusmini, PaolaGalbiati, MariaritaCristofani, RiccardoPoletti, Angelo + Article (author) -
Neuromyopathy-associated frameshift mutations in the heat shock protein b8 cause its aggregation and protostasis impairment 2025 Barbara TedescoMarta CozziValeria CrippaRiccardo CristofaniPaola RusminiVeronica FerrariElena CasarottoMarta ChierichettiPaola PramaggioreMariarita GalbiatiMargherita PiccolellaAngelo Poletti + Conference Object -
The role of CHIP in the pathogenesis of repeat expansion diseases 2025 Laura CornaggiaPaola PramaggioreMarta ChierichettiMarta CozziVeronica FerrariBarbara TedescoValeria CrippaMariarita GalbiatiMargherita PiccolellaPaola RusminiAngelo PolettiStefania MagriRiccardo Cristofani + Conference Object -
INSIGHTS INTO MITOCHONDRIAL DYSFUNCTION IN SPINAL AND BULBAR MUSCULAR ATROPHY THROUGH IPSC-DERIVED SKELETAL MUSCLE MODELS 2025 MOHAMED AliCristofani RiccardoCozzi MartaFerrari VeronicaChierichetti MartaTedesco BarbaraCrippa ValeriaRusmini PaolaPoletti AngeloGalbiati Mariarita + Conference Object -
The role of tetraspanins in extracellular vesicle-mediated clearance of insoluble TDP-43 2025 Elena CasarottoMaria BrodnanovaMarta ChierichettiLaura CornaggiaMarta CozziVeronica FerrariPrashant KoshalRocio Magdalena ParraAli MohamedMargherita PiccolellaPaola PramaggioreBarbara TedescoRiccardo CristofaniMariarita GalbiatiPaola RusminiAngelo PolettiValeria Crippa + Conference Object -
Unveiling novel players in HSPB8 pathology caused by frameshift mutations 2025 Barbara TedescoVeronica MarchesiVeronica FerrariMarta CozziPaola PramaggioreRiccardo CristofaniValeria CrippaPaola RusminiMarta ChierichettiLaura CornaggiaAli MohamedMariarita GalbiatiMargherita PiccolellaAngelo Poletti + Conference Object -
COMMON AND NOVEL MOLECULAR MECHANISMS OF FRAMESHIFT MUTATIONS CAUSING HSPB8 PATHOLOGY 2025 V. MarchesiV. FerrariM. CozziV. CrippaR. CristofaniP. PramaggioreP. RusminiM. ChierichettiL. CornaggiaA. MohamedM. GalbiatiM. PiccolellaA. PolettiB. Tedesco + Conference Object -
Unraveling the Interaction between TBP and STUB1 in the Pathogenesis of SCA17-DI 2025 Cornaggia LPramaggiore PCasarotto EChierichetti MCozzi MMohamed AFerrari VTedesco BKoshal PCrippa VGalbiati MPiccolella MRusmini PDi Bella DTaroni FPoletti ACristofani R + Conference Object -
Sex-dependent chaperone-assisted selective autophagy (CASA) activity in ALS astrocytes and microglia 2025 Barbara TedescoMarta ChierichettiMarta CozziPaola PramaggioreLaura CornaggiaMária BrodnanováElena CasarottoPrashant KoshalValeria CrippaVeronica FerrariPaola RusminiMariarita GalbiatiAli MohamedMargherita PiccolellaAngelo PolettiRiccardo Cristofani + Conference Object -
Sex-dependent chaperone-assisted selective autophagy (CASA) activity in ALS glial cells 2025 B. TedescoM. ChierichettiM. CozziV. CrippaV. FerrariP. RusminiM. GalbiatiA. PolettiR. Cristofani + Conference Object -
Interplay between GLI3 and ARpolyQ in SBMA: friend or foe? 2025 Marta CozziMaria Elena CicardiLaura CornaggiaPaola PramaggioreBarbara TedescoVeronica FerrariMarta ChierichettiMargherita PiccolellaMariarita GalbiatiPaola RusminiValeria CrippaRiccardo CristofaniAngelo Poletti + Conference Object -
Exploring the Role of CHIP in the Pathogenesis of Digenic Spinocerebellar Ataxia Type 17 2025 Laura CornaggiaPaola PramaggioreElena CasarottoMarta ChierichettiMarta CozziAli MohamedVeronica FerrariBarbara TedescoValeria CrippaMariarita GalbiatiMargherita PiccolellaPaola RusminiAngelo PolettiRiccardo Cristofani + Conference Object -
Molecular defects in KIF5A-linked neurodegenerative and neurodevelopmental diseases 2025 Cozzi MartaTedesco BarbaraPatelli GuglielmoFerrari VeronicaCasarotto ElenaChierichetti MartaPramaggiore PaolaCornaggia LauraPiccolella MargheritaGalbiati MariaritaRusmini PaolaCrippa ValeriaCristofani RiccardoPoletti Angelo + Conference Object -
Small heat shock protein B8: from cell functions to its involvement in diseases and potential therapeutic applications 2025 Chierichetti, MartaCristofani, RiccardoCrippa, ValeriaFerrari, VeronicaCozzi, MartaCasarotto, ElenaPramaggiore, PaolaCornaggia, LauraPatelli, GuglielmoMohamed, AliPiccolella, MargheritaGalbiati, MariaritaRusmini, PaolaTedesco, BarbaraPoletti, Angelo Article (author) -
Impairment of lysosomal quality control in Huntington disease 2025 Rusmini, PaolaMina, FrancescoValenza, MartaVitali, MartinaFerrari, VeronicaTedesco, BarbaraCasarotto, ElenaCozzi, MartaChierichetti, MartaMohamed, AliPramaggiore, PaolaCornaggia, LauraBrodnanova, MariaMagdalena, RocioKoshal, PrashantPiccolella, MargheritaCristofani, RiccardoGalbiati, MariaritaCrippa, ValeriaPoletti, Angelo + Article (author) -
Novel HSPB8 mutations in severe early-onset myopathy with involvement of respiratory and cardiac muscles cause proteostasis defects in cell models 2025 Tedesco, BarbaraMarchesi, VeronicaPoletti, Angelo + Article (author) -