Respiratory complications are common in the patient with muscular dystrophy. The periodic clinical and instrumental respiratory evaluation is extremely important. Despite the presence in the literature of updated guidelines, patient associations often report lack of knowledge of these pathologies, particularly in peripheral hospitals. The purpose of this work, inspired by the Italian Muscular Dystrophy Association (UILDM) is to improve management of respiratory problems necessary for the management of these patients complex. To this end, the main items that the specialist can meet in the follow-up of these pathologies have been analyzed and discussed, among which the respiratory basal evaluation, the criteria of adaptation to non-invasive ventilation, management of bronchial secretions, situations of respiratory emergency, indications for tracheostomy and the subject of advance directives of treatment (DAT).
Management of respiratory complications and rehabilitation in individuals with muscular dystrophies: 1st Consensus Conference report from UILDM - Italian Muscular Dystrophy Association (Milan, January 25-26, 2019) / F. Rao, G. Garuti, M. Vitacca, P. Banfi, F. Racca, R. Cutrera, M. Pavone, M. Pedemonte, M. Schisano, S. Pedroni, J. Casiraghi, A. Vianello, V. Sansone, G. UILDM Respiratory. - In: ACTA MYOLOGICA. - ISSN 1128-2460. - 40:1(2021), pp. 8-42. [10.36185/2532-1900-045]
|Titolo:||Management of respiratory complications and rehabilitation in individuals with muscular dystrophies: 1st Consensus Conference report from UILDM - Italian Muscular Dystrophy Association (Milan, January 25-26, 2019)|
|Parole Chiave:||Arterial blood gases; Cough efficacy; Cough machine; Invasive ventilation; Mechanical ventilation; Muscular dystrophy; Non-invasive ventilation; Polygraphy; Respiratory failure; Spirometry; Tracheostomy|
|Settore Scientifico Disciplinare:||Settore MED/26 - Neurologia|
|Data di pubblicazione:||2021|
|Digital Object Identifier (DOI):||http://dx.doi.org/10.36185/2532-1900-045|
|Appare nelle tipologie:||01 - Articolo su periodico|