Angiosarcoma is a rare malignant tumor occurring in less than 2% of soft tissue sarcomas. Angiosarcoma involving the kidney usually represents metastasis from skin or visceral primary lesions, while angiosarcoma primarily occurring in the kidney is a very rare neoplasm. In the English literature, from 1942 to the present, only 19 cases of primary kidney angiosarcoma have been reported. A case of primary renal angiosarcoma presenting as a large kidney mass and flank pain occurring after traumatism is reported. The present case represents further evidence of a rare malignancy.
Primary renal angiosarcoma: A rare malignancy. A case report and review of the literature / L. Leggio, G. Addolorato, L. Abenavoli, A. Ferrulli, C. D'Angelo, A. Mirijello, L. Vonghia, G. Schinzari, V. Arena, L. Perrone, F. Citterio, L. Bonomo, G.L. Rapaccini, A. Capelli, C. Barone, G. Gasbarrini. - In: UROLOGIC ONCOLOGY. - ISSN 1873-2496. - 24:4(2006), pp. 307-312. [10.1016/j.urolonc.2005.10.002]
Primary renal angiosarcoma: A rare malignancy. A case report and review of the literature
A. Ferrulli;
2006
Abstract
Angiosarcoma is a rare malignant tumor occurring in less than 2% of soft tissue sarcomas. Angiosarcoma involving the kidney usually represents metastasis from skin or visceral primary lesions, while angiosarcoma primarily occurring in the kidney is a very rare neoplasm. In the English literature, from 1942 to the present, only 19 cases of primary kidney angiosarcoma have been reported. A case of primary renal angiosarcoma presenting as a large kidney mass and flank pain occurring after traumatism is reported. The present case represents further evidence of a rare malignancy.File | Dimensione | Formato | |
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