Cardiac involvement in myotonic dystrophy type 1 (DM1) is frequent with an increased incidence of conduction disturbances and sudden cardiac death when compared with the general population. We described the case of a young man in whom the diagnosis of DM1 was made 8 years after the occurrence of cardiac arrest (CA) owing to ventricular fibrillation and ICD was implanted 4 years later (12 years after CA). During the subsequent 10 years, despite the deterioration of neuromuscular conditions, no appropriate or inappropriate shocks occurred.
A 10-year follow-up of a patient affected by myotonic dystrophy type 1 with implantable cardioverter-defibrillator implanted for secondary prevention / G. De Ambroggi, H. Ali, R. Cappato, V. Sansone, L. De Ambroggi. - In: JOURNAL OF CARDIOVASCULAR MEDICINE. - ISSN 1558-2027. - (2019). [Epub ahead of print]
A 10-year follow-up of a patient affected by myotonic dystrophy type 1 with implantable cardioverter-defibrillator implanted for secondary prevention
V. Sansone;L. De Ambroggi
2019
Abstract
Cardiac involvement in myotonic dystrophy type 1 (DM1) is frequent with an increased incidence of conduction disturbances and sudden cardiac death when compared with the general population. We described the case of a young man in whom the diagnosis of DM1 was made 8 years after the occurrence of cardiac arrest (CA) owing to ventricular fibrillation and ICD was implanted 4 years later (12 years after CA). During the subsequent 10 years, despite the deterioration of neuromuscular conditions, no appropriate or inappropriate shocks occurred.File | Dimensione | Formato | |
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