Purpose: To describe a multimodal imaging diagnosis of retinopathy in dermatomyositis. Case presentation: A 21-year-old white woman with a history of fatigue and a cutaneous rash complained of visual impairment in her left eye. A funduscopic examination showed multiple confluent cotton-wool spots in both eyes. Swept source-optical coherence tomography presented macular edema in both eyes; optical coherence tomography angiography revealed superficial and deep capillary occlusion in all areas affected by cotton-wool spots; and fluorescein angiography showed vascular walls enhancement, veins dilatation, and capillary leakage. After large doses of intravenously administered glucocorticoid therapy, followed by a cyclophosphamide regimen, best corrected visual acuity returned to 20/20 in both eyes. Conclusions: This case report presents optical coherence tomography angiography clinical findings in a rare case of dermatomyositis-associated retinopathy, remarking the importance of a multi-imaging approach for a correct diagnosis and treatment of eye injuries, in order to avoid serious complications and permanent sequelae.
Optical coherence tomography angiography in Purtscher-like retinopathy associated with dermatomyositis : a case report / D. Vezzola, D. Allegrini, M.R. Romano, L. Pagano, A. Montericcio, P. Fogagnolo, L.M. Rossetti, S. De Cilla. - In: JOURNAL OF MEDICAL CASE REPORTS. - ISSN 1752-1947. - 13:1(2019 Jul), pp. 206.1-206.6.
|Titolo:||Optical coherence tomography angiography in Purtscher-like retinopathy associated with dermatomyositis : a case report|
ALLEGRINI, DAVIDE (Corresponding)
FOGAGNOLO, PAOLO [Writing – Original Draft Preparation]
|Parole Chiave:||Dermatomyositis; OCTA; Retinopathy|
|Settore Scientifico Disciplinare:||Settore MED/30 - Malattie Apparato Visivo|
|Data di pubblicazione:||lug-2019|
|Digital Object Identifier (DOI):||http://dx.doi.org/10.1186/s13256-019-2152-2|
|Appare nelle tipologie:||01 - Articolo su periodico|