We describe a case of pulmonary-renal syndrome on autoimmune basis, with alveolar hemorrhage and worsening renal failure. The patient was positive for anti-MPO and anti-SCL/70. Immunosuppressive therapy was effective to treat the pulmonary condition, but chronic renal failure emerged. The clinical condition did not improve after plasmapheresis, thus chronic dialysis was required.
Viene descritto un caso di sindrome rene-polmone su base autoimmune, caratterizzata da emorragia alveolare e insufficienza renale ingravescente. La paziente è positiva per autoanticorpi anti-MPO e anti-SCL/70. Gli immunosoppressori risolvono il quadro polmonare ma si hanno esiti di insufficienza renale cronica. La plasmaferesi non migliora il quadro clinico e si rende necessario un trattamento dialitico cronico.
Un caso di emorragia alveolare in sindrome rene-polmone anti-mieloperossidasi e anti-SCL/70 positiva / C. Defendenti, M.F. Spina, A. Castiglione, F. Atzeni, A. Miadonna, M. Saudelli, G. Guercilena, P. Sarzi-Puttini. - In: RECENTI PROGRESSI IN MEDICINA. - ISSN 0034-1193. - 100:7-8(2009 Jul), pp. 361-364. [10.1701/444.5235]
Un caso di emorragia alveolare in sindrome rene-polmone anti-mieloperossidasi e anti-SCL/70 positiva
M.F. Spina;P. Sarzi-Puttini
2009
Abstract
We describe a case of pulmonary-renal syndrome on autoimmune basis, with alveolar hemorrhage and worsening renal failure. The patient was positive for anti-MPO and anti-SCL/70. Immunosuppressive therapy was effective to treat the pulmonary condition, but chronic renal failure emerged. The clinical condition did not improve after plasmapheresis, thus chronic dialysis was required.Pubblicazioni consigliate
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