Weber-Christian Disease (WCD), also known as relapsing febrile lobular non-suppurative panniculitis, is a rare condition characterized by recurrent subcutaneous inflammatory nodules in the adipose tissue in addition to fever, malaise and other systemic manifestations such as polyarthralgia and polymyalgia. The association with small vessel vasculitis has been rarely reported. We report here an unusual case of WCD associated with small vessels vasculitis also describing the efficacy of Cyclosporin A treatment.
Efficacy of cyclosporine A treatment in relapsing febrile lobular panniculitis associated with small vessel vasculitis / L. Cantarini, F. Fanti, M. Galeazzi, S. Martino, C. Miracco, M. Biagioli, N. Dal Canto, R. Cimaz. - In: RHEUMATOLOGY INTERNATIONAL. - ISSN 0172-8172. - 30:6(2010), pp. 797-799.
Efficacy of cyclosporine A treatment in relapsing febrile lobular panniculitis associated with small vessel vasculitis
R. Cimaz
2010
Abstract
Weber-Christian Disease (WCD), also known as relapsing febrile lobular non-suppurative panniculitis, is a rare condition characterized by recurrent subcutaneous inflammatory nodules in the adipose tissue in addition to fever, malaise and other systemic manifestations such as polyarthralgia and polymyalgia. The association with small vessel vasculitis has been rarely reported. We report here an unusual case of WCD associated with small vessels vasculitis also describing the efficacy of Cyclosporin A treatment.File | Dimensione | Formato | |
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