We report the case of a 46-year-old woman presenting cutaneous lesions similar to those of pityriasis rubra pilaris, characterized by diffuse scaling erythroderma and palmoplantar keratoderma; skin biopsy showed follicular hyperkeratosis with a perivascular lymphocytic infiltrate. One year later she developed an inflammatory myopathy; on the basis of clinical features, a diagnosis of dermatomyositis was made. Treatment with prednisone and hydroxychloroquine led to complete control of the cutaneous and muscular involvement, which was maintained during prednisone tapering
Inflammatory myopathy in a patient with cutaneous findings of pityriasis rubra pilaris: a case of wong's dermatomyositis / R. Caporali, L. Cavagna, M. Bellosta, L. Bogliolo, C. Montecucco. - In: CLINICAL RHEUMATOLOGY. - ISSN 0770-3198. - 23:1(2004), pp. 63-65.
Inflammatory myopathy in a patient with cutaneous findings of pityriasis rubra pilaris: a case of wong's dermatomyositis
R. Caporali;
2004
Abstract
We report the case of a 46-year-old woman presenting cutaneous lesions similar to those of pityriasis rubra pilaris, characterized by diffuse scaling erythroderma and palmoplantar keratoderma; skin biopsy showed follicular hyperkeratosis with a perivascular lymphocytic infiltrate. One year later she developed an inflammatory myopathy; on the basis of clinical features, a diagnosis of dermatomyositis was made. Treatment with prednisone and hydroxychloroquine led to complete control of the cutaneous and muscular involvement, which was maintained during prednisone taperingFile | Dimensione | Formato | |
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