Inherited epidermolysis bullosa (EB) is a clinically and genetically heterogeneous group of rare diseases characterized by skin and mucous membrane fragility. EB primarily involves the skin and, in specific subtypes, the mucous membrane, resulting in complications which can strongly affect nutritional status (e.g. gastrointestinal complications, hand deformities, pain). The aims of nutritional support mainly include improving nutritional status, alleviating the stress of oral feeding and minimizing nutritional deficiencies, thus consequently improving growth, pubertal development, bowel function, immune status and wound healing. The aim of this review is to discuss knowledge of different aspects of the disease related to nutrition and growth.

A nutrition-based approach to epidermolysis bullosa: Causes, assessments, requirements and management / S. Salera, G. Tadini, D. Rossetti, F.S. Grassi, P. Marchisio, C. Agostoni, C. Giavoli, G. Rodari, S. Guez. - In: CLINICAL NUTRITION. - ISSN 0261-5614. - (2019). [Epub ahead of print] [10.1016/j.clnu.2019.02.023]

A nutrition-based approach to epidermolysis bullosa: Causes, assessments, requirements and management

D. Rossetti;F.S. Grassi;P. Marchisio;C. Agostoni;C. Giavoli;G. Rodari
Penultimo
;
2019

Abstract

Inherited epidermolysis bullosa (EB) is a clinically and genetically heterogeneous group of rare diseases characterized by skin and mucous membrane fragility. EB primarily involves the skin and, in specific subtypes, the mucous membrane, resulting in complications which can strongly affect nutritional status (e.g. gastrointestinal complications, hand deformities, pain). The aims of nutritional support mainly include improving nutritional status, alleviating the stress of oral feeding and minimizing nutritional deficiencies, thus consequently improving growth, pubertal development, bowel function, immune status and wound healing. The aim of this review is to discuss knowledge of different aspects of the disease related to nutrition and growth.
Enteral nutrition; Epidermolysis bullosa; Growth retardation; Hypercatabolism; Nutritional status; Undernutrition
Settore MED/38 - Pediatria Generale e Specialistica
Settore MED/13 - Endocrinologia
2019
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/2434/652330
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