Acquired deficiency of the inhibitor of the first complement component (C1-INH) is a rare, potentially life-threatening disease whose cause, course, and management are not completely defined. This article analyzes the etiopathogenetic mechanism, the clinical presentation, and the relationship between acquired C1-INH deficiency and lymphoproliferative disorders. Moreover, the authors give an overview of the outcome of the disease and the different therapies proposed to cure it.
Acquired deficiency of the inhibitor of the first complement component : presentation, diagnosis, course, and conventional management / L.C. Zingale, R. Castelli, A. Zanichelli, M. Cicardi. - In: IMMUNOLOGY AND ALLERGY CLINICS OF NORTH AMERICA. - ISSN 0889-8561. - 26:4(2006 Nov), pp. 669-690.
Acquired deficiency of the inhibitor of the first complement component : presentation, diagnosis, course, and conventional management
L.C. Zingale;R. Castelli;A. Zanichelli;M. Cicardi
2006
Abstract
Acquired deficiency of the inhibitor of the first complement component (C1-INH) is a rare, potentially life-threatening disease whose cause, course, and management are not completely defined. This article analyzes the etiopathogenetic mechanism, the clinical presentation, and the relationship between acquired C1-INH deficiency and lymphoproliferative disorders. Moreover, the authors give an overview of the outcome of the disease and the different therapies proposed to cure it.Pubblicazioni consigliate
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