In the present study, a modification has been proposed of the Blauth and Gekeler classification, aimed at a more accurate definition of appropriate surgical treatment. An analysis was made of a series of 120 cases of symbrachydactyly (117 patients); however, surgery was only performed in 86 cases (51 toe transfers in 49 patients; mean age at surgery 12 months). Type I included the separation of short and sometimes stiff fingers; type II, the 'pseudo-cleft', could be subdivided into three groups. Type IIA included those hands with more than two long and frequently hypoplastic digits, regarding which a decision had to be made between removal of rudimentary fingers or their stabilization. In type IIB, hand function was good and surgery was rarely needed. Type III (monodactylous) could also be subdivided into two categories, i.e., normal thumb in type IIIA and hypoplasia in IIIB. Finally, in type IVA, toe transfer surgery was performed on condition that wrist mobility was sufficient to compensate for the insufficient mobility of the artificial thumb on the anterior aspect of the radius. In all cases, a weak but useful pincer movement was obtained, with poor cosmetic results. In the case of toe transfers, surgery was advocated before the age of one year; and although mobility was disappointing (35 degrees active motion), good growth and excellent discrimination (5 mm on average) was observed. Symbrachydactyly is a fairly frequent congenital malformation; its diverse clinical features require a precise classification to better determine adequate treatment management.

La symbrachydactylie, classification et traitement : À propos d'une série de 117 cas / G. Foucher, J. Medina, G. Pajardi, R. Navarro. - In: CHIRURGIE DE LA MAIN. - ISSN 1297-3203. - 19:3(2000 Jul), pp. 161-168. [10.1016/S1297-3203(00)73475-5]

La symbrachydactylie, classification et traitement : À propos d'une série de 117 cas

G. Pajardi
Penultimo
;
2000

Abstract

In the present study, a modification has been proposed of the Blauth and Gekeler classification, aimed at a more accurate definition of appropriate surgical treatment. An analysis was made of a series of 120 cases of symbrachydactyly (117 patients); however, surgery was only performed in 86 cases (51 toe transfers in 49 patients; mean age at surgery 12 months). Type I included the separation of short and sometimes stiff fingers; type II, the 'pseudo-cleft', could be subdivided into three groups. Type IIA included those hands with more than two long and frequently hypoplastic digits, regarding which a decision had to be made between removal of rudimentary fingers or their stabilization. In type IIB, hand function was good and surgery was rarely needed. Type III (monodactylous) could also be subdivided into two categories, i.e., normal thumb in type IIIA and hypoplasia in IIIB. Finally, in type IVA, toe transfer surgery was performed on condition that wrist mobility was sufficient to compensate for the insufficient mobility of the artificial thumb on the anterior aspect of the radius. In all cases, a weak but useful pincer movement was obtained, with poor cosmetic results. In the case of toe transfers, surgery was advocated before the age of one year; and although mobility was disappointing (35 degrees active motion), good growth and excellent discrimination (5 mm on average) was observed. Symbrachydactyly is a fairly frequent congenital malformation; its diverse clinical features require a precise classification to better determine adequate treatment management.
Afin de faciliter les indications chirurgicales, nous proposons une modification de la classification des symbrachydactylies (Blauth). Sur 120 symbrachydactylies (117 patients), 86 mains ont été opérées. La libération commissurale a été le geste le plus fréquent (81 espaces). Le transfert d’orteil a été réservé aux formes sévères monodactyles ou adactyles (51 transferts chez 49 patients opérés à un âge moyen de 12 mois). Le type I nécessite la séparation de doigts courts et parfois raides. Le type II, « pseudo-fourche », doit être divisé en trois sous-groupes. Si le groupe IIC, avec main en cuillère est rare, le type IIA, avec plus de deux doigts longs, souvent hypoplasiques et instables, doit faire choisir entre le sacrifice de doigts rudimentaires et leur stabilisation. Le type IIB nécessite rarement une intervention car la prise est souvent excellente. Le type III monodactyle mérite d’être séparé en type IIIA avec pouce normal et IIIB avec instabilité et hypoplasie. Enfin le type péromélique est accessible à un transfert d’orteil en position antébrachiale, à condition que la mobilité du poignet (type IVA) compense l’insuffisance de celle du transfert. En cas d’indication de transfert d’orteil, l’intervention pratiquée avant l’âge d’un an permet une intégration excellente. Si la mobilité active a été décevante (en moyenne 35°), la croissance a été bonne et la sensibilité excellente(discrimination moyenne de 5 mm). La symbrachydactylie est une entité qui est intégrée au groupe I (classification de l’IFSSH). La variété de présentation nécessite une classification précise afin d’affiner les indications chirurgicales.
Congenital malformation; Hand; Symbrachydactyly; Toe transfer; Transverse deficiency
Settore MED/19 - Chirurgia Plastica
lug-2000
Article (author)
File in questo prodotto:
File Dimensione Formato  
1-s2.0-S1297320300734755-main.pdf

accesso riservato

Tipologia: Publisher's version/PDF
Dimensione 1.08 MB
Formato Adobe PDF
1.08 MB Adobe PDF   Visualizza/Apri   Richiedi una copia
Pubblicazioni consigliate

I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.

Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/2434/442614
Citazioni
  • ???jsp.display-item.citation.pmc??? 3
  • Scopus 12
  • ???jsp.display-item.citation.isi??? ND
social impact