Objectives Binder syndrome is an uncommon disorder of unknown etiology. It is characterized by hypoplasia of the nose and maxilla and altered morphology of the associated soft tissues. The authors report the case of a 10-year-old Binder syndrome patient with short-nose deformity and anterior nasal spine hypoplasia. Materials and Methods The patient was initially treated with a TSME (Transverse Sagittal Maxillary Expander) to correct the maxillary hypoplasia and subsequently with a fixed appliance therapy to achieve esthetic goals. At the end of the orthodontic treatment, a maxillofacial surgery was performed to correct the nasal hypoplasia. Conclusions A multidisciplinary approach, including also the orthodontic treatment, is necessary to solve the alterations occurring in Binder syndrome.
Obiettivi La sindrome di Binder è un raro disordine di eziologa sconosciuta, caratterizzato da ipoplasia del naso e del mascellare superiore e dall’alterazione della morfologia dei tessuti molli associati. Gli autori riportano il caso di una paziente di 10 anni affetta da sindrome di Binder, con naso corto e ipoplasia della spina nasale anteriore. Materiali e Metodi La paziente è stata trattata prima con TSME (Transverse Sagittal Maxillary Expander) per correggere l’ipoplasia del mascellare e successivamente con terapia fissa per ottenere i risultati estetici. Alla fine del trattamento ortodontico è stata effettuata la chirurgia maxillofacciale per correggere l’ipoplasia nasale. Conclusioni Un approccio multidisciplinare, che comprenda anche la terapia ortodontica, è necessario per risolvere le alterazioni presenti nella sindrome di Binder.
Sindrome di Binder: caso clinico=Binder syndrome: a case report / G. Farronato, C. Folegatti, L. Giannini, G. Galbiati, S. Pelo, C. Maspero. - In: DENTAL CADMOS. - ISSN 0011-8524. - 82:3(2014), pp. 205-215. [10.1016/S0011-8524(14)70152-7]
Sindrome di Binder: caso clinico=Binder syndrome: a case report
G. Farronato
;C. Maspero
2014
Abstract
Objectives Binder syndrome is an uncommon disorder of unknown etiology. It is characterized by hypoplasia of the nose and maxilla and altered morphology of the associated soft tissues. The authors report the case of a 10-year-old Binder syndrome patient with short-nose deformity and anterior nasal spine hypoplasia. Materials and Methods The patient was initially treated with a TSME (Transverse Sagittal Maxillary Expander) to correct the maxillary hypoplasia and subsequently with a fixed appliance therapy to achieve esthetic goals. At the end of the orthodontic treatment, a maxillofacial surgery was performed to correct the nasal hypoplasia. Conclusions A multidisciplinary approach, including also the orthodontic treatment, is necessary to solve the alterations occurring in Binder syndrome.File | Dimensione | Formato | |
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