Primary intestinal lymphangiectasia (PIL) is a protein-losing enteropathy characterized by tortuous and dilated lymph channels of the small bowel. The main symptoms are bilateral lower limb edema, serosal effusions, vitamin D malabsorption resulting in osteoporosis. We reported here a case of long-lasting misdiagnosed PIL with a peculiar liver picture, characterized by very high stiffness value at transient elastography, which decreased with clinical improvement. The complex interplay between lymphatic and hepatic circulatory system was discussed
Intestinal lymphangiectasia and reversible high liver stiffness / L. Milazzo , A. M. Peri , L. Lodi , G. Gubertini , A. L. Ridolfo , S. Antinori. - In: HEPATOLOGY. - ISSN 0270-9139. - 60:2(2014 Jan), pp. 759-761. [Epub ahead of print] [10.1002/hep.27025]
Intestinal lymphangiectasia and reversible high liver stiffness
S. Antinori
2014
Abstract
Primary intestinal lymphangiectasia (PIL) is a protein-losing enteropathy characterized by tortuous and dilated lymph channels of the small bowel. The main symptoms are bilateral lower limb edema, serosal effusions, vitamin D malabsorption resulting in osteoporosis. We reported here a case of long-lasting misdiagnosed PIL with a peculiar liver picture, characterized by very high stiffness value at transient elastography, which decreased with clinical improvement. The complex interplay between lymphatic and hepatic circulatory system was discussedPubblicazioni consigliate
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