Kaposiform hemangioendothelioma is a rare vascular neoplasm in children often associated with Kasabach-Merritt syndrome. The tumor usually presents in retroperitoneal location and is rarely present at birth. Cutaneous lesions manifest after birth and must be clinically differentiated from infantile hemangiomas and diffuse neonatal hemangiomatosis. Histologically, it bears similarities with Kaposi sarcoma. We present a case of congenital cutaneous multifocal kaposiform hemangioendothelioma (KHE).

Congenital cutaneous multifocal kaposiform hemangioendothelioma / R. Gianotti, C. Gelmetti, E. Alessi. - In: AMERICAN JOURNAL OF DERMATOPATHOLOGY. - ISSN 0193-1091. - 21:6(1999 Dec), pp. 557-561.

Congenital cutaneous multifocal kaposiform hemangioendothelioma

R. Gianotti
Primo
;
C. Gelmetti
Secondo
;
1999

Abstract

Kaposiform hemangioendothelioma is a rare vascular neoplasm in children often associated with Kasabach-Merritt syndrome. The tumor usually presents in retroperitoneal location and is rarely present at birth. Cutaneous lesions manifest after birth and must be clinically differentiated from infantile hemangiomas and diffuse neonatal hemangiomatosis. Histologically, it bears similarities with Kaposi sarcoma. We present a case of congenital cutaneous multifocal kaposiform hemangioendothelioma (KHE).
Children; Congenital vascular neoplasms; Vascular neoplasms
Settore MED/35 - Malattie Cutanee e Veneree
Settore MED/08 - Anatomia Patologica
dic-1999
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/2434/200224
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