Neuromuscular diseases (NMDs) comprise a heterogeneous group of conditions characterized by extreme progressive muscle weakness leading to respiratory failure. Noninvasive mechanical ventilation (NIV) has emerged as a cornerstone in the management of respiratory complications associated with NMDs. This review aims to elucidate the role of NMV in respiratory function, improving quality of life, and prolonging survival in individuals with NMD. The physiological basis of respiratory impairment in NMDs, principles of NMV application, evidence supporting its efficacy, patient selection criteria, and potential challenges in its application are discussed.

Enhancing respiratory function in neuromuscular disease: the role of non-invasive ventilation. A narrative review / P. Banfi, A.A.M.D.B.. - In: ACTA MYOLOGICA. - ISSN 2532-1900. - 43:2(2024 Jun 30), pp. 78-82. [10.36185/2532-1900-506]

Enhancing respiratory function in neuromuscular disease: the role of non-invasive ventilation. A narrative review

A.A.M.D. Buscemi
Secondo
;
M. Mantero
Penultimo
;
2024

Abstract

Neuromuscular diseases (NMDs) comprise a heterogeneous group of conditions characterized by extreme progressive muscle weakness leading to respiratory failure. Noninvasive mechanical ventilation (NIV) has emerged as a cornerstone in the management of respiratory complications associated with NMDs. This review aims to elucidate the role of NMV in respiratory function, improving quality of life, and prolonging survival in individuals with NMD. The physiological basis of respiratory impairment in NMDs, principles of NMV application, evidence supporting its efficacy, patient selection criteria, and potential challenges in its application are discussed.
neuromuscular diseases; non-invasive ventilation; quality of life; respiratory failure; survival;
Settore MEDS-07/A - Malattie dell'apparato respiratorio
30-giu-2024
29-mag-2024
https://www.actamyologica.it/article/view/506
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/2434/1266395
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