Background: Acquired von Willebrand syndrome (AVWS) is a rare bleeding disorder due to reduced or dysfunctional VWF in individuals without a personal or familial bleeding history. It is associated with systemic diseases such as lymphoproliferative (LPDs) and myeloproliferative neoplasms (MPNs), cardiovascular, and autoimmune conditions. The underlying biological processes differ across clinical contexts and remain incompletely defined, complicating both diagnosis and management.
Clinical and Laboratory Characterization of Acquired Von Willebrand Syndrome / A. Ciavarella ; tutor: F. Peyvandi ; coordinator: M. S. Clerici. Dipartimento di Fisiopatologia Medico-Chirurgica e dei Trapianti, 2025 Jun 18. 36. ciclo, Anno Accademico 2022/2023.
CLINICAL AND LABORATORY CHARACTERIZATION OF ACQNIREA VON WILLEBRAND SYLARORE.
A. Ciavarella
2025
Abstract
Background: Acquired von Willebrand syndrome (AVWS) is a rare bleeding disorder due to reduced or dysfunctional VWF in individuals without a personal or familial bleeding history. It is associated with systemic diseases such as lymphoproliferative (LPDs) and myeloproliferative neoplasms (MPNs), cardiovascular, and autoimmune conditions. The underlying biological processes differ across clinical contexts and remain incompletely defined, complicating both diagnosis and management.| File | Dimensione | Formato | |
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