Sickle cell disease (SCD) refers to a group of hereditary disorders associated with clinical manifestations of variable severity. C In particular, Fat Embolism Syndrome, a rare and devastating complication of SCD, may preferentially involve non-homozygous patients and patients with mild disease.
A Suspected Case of Cerebral Fat Embolism Triggering a Drug-resistant Status Epilepticus in a HbS/β+-Thalassaemia Patient / M. Bortolotti, G. Costamagna, D. Gagliardi, M.M. De Amicis, N. Bresolin, G. Graziadei. - In: MEDITERRANEAN JOURNAL OF HEMATOLOGY AND INFECTIOUS DISEASES. - ISSN 2035-3006. - 14:1(2022 Feb), pp. e2022019.1-e2022019.3. [10.4084/MJHID.2022.019]
A Suspected Case of Cerebral Fat Embolism Triggering a Drug-resistant Status Epilepticus in a HbS/β+-Thalassaemia Patient
M. BortolottiCo-primo
Conceptualization
;G. CostamagnaCo-primo
Conceptualization
;D. Gagliardi;N. Bresolin;
2022
Abstract
Sickle cell disease (SCD) refers to a group of hereditary disorders associated with clinical manifestations of variable severity. C In particular, Fat Embolism Syndrome, a rare and devastating complication of SCD, may preferentially involve non-homozygous patients and patients with mild disease.| File | Dimensione | Formato | |
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