Sickle cell disease (SCD) refers to a group of hereditary disorders associated with clinical manifestations of variable severity. C In particular, Fat Embolism Syndrome, a rare and devastating complication of SCD, may preferentially involve non-homozygous patients and patients with mild disease. 

A Suspected Case of Cerebral Fat Embolism Triggering a Drug-resistant Status Epilepticus in a HbS/β+-Thalassaemia Patient / M. Bortolotti, G. Costamagna, D. Gagliardi, M.M. De Amicis, N. Bresolin, G. Graziadei. - In: MEDITERRANEAN JOURNAL OF HEMATOLOGY AND INFECTIOUS DISEASES. - ISSN 2035-3006. - 14:1(2022 Feb), pp. e2022019.1-e2022019.3. [10.4084/MJHID.2022.019]

A Suspected Case of Cerebral Fat Embolism Triggering a Drug-resistant Status Epilepticus in a HbS/β+-Thalassaemia Patient

M. Bortolotti
Co-primo
Conceptualization
;
G. Costamagna
Co-primo
Conceptualization
;
D. Gagliardi;N. Bresolin;
2022

Abstract

Sickle cell disease (SCD) refers to a group of hereditary disorders associated with clinical manifestations of variable severity. C In particular, Fat Embolism Syndrome, a rare and devastating complication of SCD, may preferentially involve non-homozygous patients and patients with mild disease. 
sickle cell disease; cerebral fat embolism; status epilepticus; eritroexchange
Settore MEDS-09/B - Malattie del sangue
feb-2022
Article (author)
File in questo prodotto:
File Dimensione Formato  
Cerebral_Fat_embolism_Bortolotti_MJHID_2022.pdf

accesso aperto

Tipologia: Publisher's version/PDF
Licenza: Creative commons
Dimensione 1.44 MB
Formato Adobe PDF
1.44 MB Adobe PDF Visualizza/Apri
Pubblicazioni consigliate

I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.

Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/2434/1172433
Citazioni
  • ???jsp.display-item.citation.pmc??? ND
  • Scopus 0
  • ???jsp.display-item.citation.isi??? 1
  • OpenAlex ND
social impact