DOBI, DORINA
DOBI, DORINA
Dipartimento di Biotecnologie Mediche e Medicina Traslazionale
GM1 oligosaccharide-mediated rescue in GBA-linked Parkinson’s disease via modulation of lysosomal and mitochondrial dysfunctions
2025 G. Lunghi, C. Pedroli, I. Tagliabue, D. Dobi, M.G. Ciampa, L. Mauri, L. Rouvière, A. Henriques, N. Callizot, S. Sonnino, E. Chiricozzi, M. Fazzari
Mapping the Impact of ETI-mediated CFTR Reactivation On Development: a zebrafish model study
2025 M. Cafora, S. Pagliughi, D. Dobi, G. Galassi, A. Mantero, M. Aureli, A. Pistocchi
Metabolic and Structural Consequences of GM3 Synthase Deficiency: Insights from an HEK293-T Knockout Model
2025 E. Chiricozzi, G. Lunghi, M. Valsecchi, E.V. Carsana, R. Bassi, E. Di Biase, D. Dobi, M.G. Ciampa, L. Mauri, M. Aureli, K. Inamori, J. Inokuchi, S. Sonnino, M. Fazzari
Effect of CFTR modulators Elexacaftor/Tezacaftor/Ivacaftor on lipid metabolism in human bronchial epithelial cells
2025 D. Dobi, N. Loberto, L. Mauri, R. Bassi, E. Chiricozzi, G. Lunghi, M. Aureli
Effects of GM1 ganglioside and its derivatives on ETI-rescued F508del-CFTR maturation and host-pathogen interactions in cystic fibrosis bronchial cells
2025 D. Dobi, A. Rimessi, N. Loberto, L. Mauri, R. Bassi, E. Chiricozzi, D. Olioso, G. Pellielo, P. Pinton, V. Bezzerri, G. Cabrini, G. Lippi, A. Tamanini, G. Lunghi, M. Aureli
Anti-inflammatory activity of Pseudomonas aeruginosa DEV phage in cystic fibrosis models
2025 M. Cafora, D. Dobi, J.N.G. William, F. Forti, L. Belleri, N. Loberto, R. Bassi, S. Carbone, M. Locati, M. Aureli, F. Briani, A. Pistocchi
Tezacaftor is a direct inhibitor of sphingolipid delta-4 desaturase enzyme (DEGS)
2024 D.Z. Ciobanu, N. Liessi, V. Tomati, V. Capurro, S.M. Bertozzi, M. Summa, R. Bertorelli, N. Loberto, D. Dobi, M. Aureli, L. Nobbio, T. Bandiera, N. Pedemonte, R. Bassi, A. Armirotti
LIPID-BASED APPROACHES TO OPTIMIZE THE EFFECTIVENESS OF INNOVATIVE DRUG MODULATORS IN CYSTIC FIBROSIS
2024 D. Dobi
Cross‐talk between CFTR and sphingolipids in cystic fibrosis
2023 D. Dobi, N. Loberto, R. Bassi, A.S. Pistocchi, G. Lunghi, A. Tamanini, M. Aureli
Gangliosides and Cell Surface Ganglioside Metabolic Enzymes in the Nervous System
2022 M. Aureli, L. Mauri, E.V. Carsana, D. Dobi, S. Breviario, G. Lunghi, S. Sonnino