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Mostrati risultati da 21 a 40 di 98
Titolo Data di pubblicazione Autori Tipo File Abstract
Tdp-25 Routing to Autophagy and Proteasome Ameliorates its Aggregation in Amyotrophic Lateral Sclerosis Target Cells 2018 Cicardi, Maria ElenaCristofani, RiccardoRusmini, PaolaMeroni, MarcoFerrari, VeronicaTedesco, BarbaraPiccolella, MargheritaMessi, ElioGalbiati, MariaritaBoncoraglio, AlessandraCrippa, ValeriaPoletti, Angelo + Article (author) -
Characterization of two new mutations in the small Heat Shock protein B8 HSPB8 and impact in Amyotrophic Lateral Sclerosis cell models 2018 barbara tedescovaleria cripparusmini paolacristofani riccardocicardi maria elenaferrari veronicameroni marcomessi eliopiccolella margheritagalbiati ritapoletti angelo + Conference Object -
Novel role of VCP in the clearance of mutant-SOD1 in als 2018 Ferrari V.Cicardi M. E.Crippa V.Rusmini P.Cristofani R.Meroni M.Tedesco B.Galbiati M.Poletti A. Conference Object -
VCP: a novel regulator of SOD1-G93A clearance in a als model 2018 Ferrari V.Cicardi M. E.Crippa V.Rusmini P.Cristofani R.Meroni M.Tedesco B.Galbiati M.Poletti A Conference Object -
New HSPB8 mutations related to Amyotrophic Lateral Sclerosis : characterization and impact in cell models of disease 2018 tedesco barbaracrippa valeriarusmini paolacristofani riccardocicardi maria elenaferrari veronicameroni marcomessi eliopiccolella margheritagalbiati ritapoletti angelo + Conference Object -
Chaperone Assisted Selective Autophagy (CASA) a potential target for therapeutics in motoneuron diseases 2018 Crippa V.Rusmini P.Cristofani R.Cicardi M. E.Meroni M.Ferrari V.Tedesco B.Piccolella M.Messi E.Galbiati M.Poletti A. Conference Object -
Chaperone mediated autophagy respond to dynein mediated transport inhibition in motor neuron diseases 2018 Riccardo CristofaniValeria CrippaMaria Elena CicardiPaola RusminiMarco MeroniVeronica FerrariTEDESCO, BARBARAMariarita GalbiatiAngelo Poletti + Conference Object -
The small heat shock protein B8 at the interplay between the intracellular degradative pathways in motoneuron disease 2018 A. POLETTIR. CRISTOFANIV. CRIPPAP. RUSMINIV. FERRARIB. TEDESCOM. MERONIM. GALBIATI + Conference Object -
Chaperone mediated autophagy responds to macroautophagy inhibition in motor neuron diseases 2018 Riccardo CristofaniValeria CrippaMaria Elena CicardiPaola RusminiMarco MeroniVeronica FerrariBarbara TedescoMariarita GalbiatiElio MessiMargherita PiccolellaAngelo Poletti + Conference Object -
The small heat shock protein B8 (HSPB8) removes dipeptides produced in C9ORF72-related neurodegenerative diseases 2018 Cristofani RCrippa VCicardi MERusmini PMeroni MFerrari VTedesco BMessi EPiccolella MGalbiati MPoletti A + Conference Object -
Identification of new HSPB8 variants linked to familial Amiotrophic Lateral Sclerosis 2018 V. CrippaB. TedescoM. E. CicardiP. RusminiR. CristofaniV. FerrariM. MeroniE. MessiM. PiccolellaM. GalbiatiN. TicozziA. RattiV. SilaniA . Poletti + Conference Object -
TDP25 aggregation in motor neuron and muscle cells is rescued by chaperone overexpression 2018 M. E. CicardiR. CristofaniP. RusminiM. MeroniV. FerrariB. TedescoM. GalbiatiV. CrippaA. Poletti. + Conference Object -
Trehalose induces autophagy via lysosomal-mediated TFEB activation in models of motoneuron degeneration 2018 P. RusminiK. CorteseV. CrippaR. CristofaniM. E. CicardiV. FerrariG. VezzoliB. TedescoM. MeroniE. MessiM. PiccolellaM. GalbiatiE. MorelliT. VaccariA. Poletti + Article (author) -
ALS-associeted VCP-mutants lead to lysosome damage 2019 V. FerrariP. RusminiV. CrippaR. CristofaniB. TedescoM. GalbiatiE. MessiM. PiccolellaA. Poletti + Conference Object -
Transcriptional alterations induced by polyDPRs overexpression in neuronal cell model 2019 Cristofani R. )Crippa V.Rusmini P.Tedesco B.Ferrari V.CASAROTTO, ELENAGalbiati M.Poletti A. + Conference Object -
Novel pathogenic mechanism of ALS-associated VCP- mutants 2019 V. FerrariP. RusminiV. CrippaR. CristofaniB. TedescoM. GalbiatiE. MessiM. PiccolellaA. Poletti + Conference Object -
The clearance of aggregated TDP-43 responsible for ALS/FTD diseases 2019 V. CrippaM. E. CicardiE. CasarottoB. TedescoR. CristofaniV. FerrariM. ChierichettiP. RusminiM. GalbiatiM. PiccolellaE. MessiA. Poletti + Conference Object -
The regulation of the small heat shock protein B8 in misfolding protein diseases causing motoneuronal and muscle cell death 2019 Cristofani, RiccardoRusmini, PaolaGalbiati, MariaritaCicardi, Maria ElenaFerrari, VeronicaTedesco, BarbaraCasarotto, ElenaChierichetti, MartaMessi, ElioPiccolella, MargheritaCrippa, ValeriaPoletti, Angelo + Article (author) -
Autophagic and Proteasomal Mediated Removal of Mutant Androgen Receptor in Muscle Models of Spinal and Bulbar Muscular Atrophy 2019 Cicardi, Maria ElenaCristofani, RiccardoCrippa, ValeriaFerrari, VeronicaTedesco, BarbaraCasarotto, ElenaChierichetti, MartaGalbiati, MariaritaPiccolella, MargheritaMessi, ElioRusmini, PaolaPoletti, Angelo + Article (author) -
C9ORF72 arginine rich poly-dipeptides induce transcriptional alterations in ALS/FTD cell model 2019 Riccardo CristofaniAndrea GrilliValeria CrippaMaria Elena CicardiPaola RusminiBarbara TedescoVeronica FerrariElena CasarottoMarta ChierichettiMariarita GalbiatiAngelo Poletti + Conference Object -
Mostrati risultati da 21 a 40 di 98
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