Sfoglia per Autore
Tdp-25 Routing to Autophagy and Proteasome Ameliorates its Aggregation in Amyotrophic Lateral Sclerosis Target Cells
2018 M.E. Cicardi, R. Cristofani, P. Rusmini, M. Meroni, V. Ferrari, G. Vezzoli, B. Tedesco, M. Piccolella, E. Messi, M. Galbiati, A. Boncoraglio, S. Carra, V. Crippa, A. Poletti
Characterization of two new mutations in the small Heat Shock protein B8 HSPB8 and impact in Amyotrophic Lateral Sclerosis cell models
2018 B. Tedesco, V. Crippa, P. Rusmini, R. Cristofani, M.E. Cicardi, V. Ferrari, G. Vezzoli, M. Meroni, E. Messi, M. Piccolella, R. Galbiati, A. Poletti
Novel role of VCP in the clearance of mutant-SOD1 in als
2018 V. Ferrari, M.E. Cicardi, V. Crippa, P. Rusmini, R. Cristofani, M. Meroni, B. Tedesco, M. Galbiati, A. Poletti
VCP: a novel regulator of SOD1-G93A clearance in a als model
2018 V. Ferrari, M.E. Cicardi, V. Crippa, P. Rusmini, R. Cristofani, M. Meroni, B. Tedesco, M. Galbiati, A. Poletti
New HSPB8 mutations related to Amyotrophic Lateral Sclerosis : characterization and impact in cell models of disease
2018 B. Tedesco, V. Crippa, P. Rusmini, R. Cristofani, M.E. Cicardi, V. Ferrari, G. Vezzoli, M. Meroni, E. Messi, M. Piccolella, R. Galbiati, A. Poletti
Chaperone Assisted Selective Autophagy (CASA) a potential target for therapeutics in motoneuron diseases
2018 V. Crippa, P. Rusmini, R. Cristofani, M.E. Cicardi, M. Meroni, V. Ferrari, B. Tedesco, M. Piccolella, E. Messi, M. Galbiati, A. Poletti
Chaperone mediated autophagy respond to dynein mediated transport inhibition in motor neuron diseases
2018 R.M. Cristofani, V. Crippa, M.E. Cicardi, P. Rusmini, M. Meroni, V. Ferrari, B. Tedesco, M. Galbiati, S. Gessica, F. Carlo, A. Poletti
The small heat shock protein B8 at the interplay between the intracellular degradative pathways in motoneuron disease
2018 A. Poletti, R. Cristofani, V. Crippa, P. Rusmini, M.E. Cicardi, V. Ferrari, B. Tedesco, M. Meroni, M. Galbiati, S. Cerra
Chaperone mediated autophagy responds to macroautophagy inhibition in motor neuron diseases
2018 R.M. Cristofani, V. Crippa, M.E. Cicardi, P. Rusmini, M. Meroni, V. Ferrari, B. Tedesco, M. Galbiati, E. Messi, M. Piccolella, G. Sala, C. Ferrarese, A. Poletti
The small heat shock protein B8 (HSPB8) removes dipeptides produced in C9ORF72-related neurodegenerative diseases
2018 R. Cristofani, V. Crippa, M. Cicardi, P. Rusmini, M. Meroni, V. Ferrari, B. Tedesco, E. Messi, M. Piccolella, M. Galbiati, S. Carra, A. Poletti
Identification of new HSPB8 variants linked to familial Amiotrophic Lateral Sclerosis
2018 V. Crippa, B. Tedesco, M.E. Cicardi, P. Rusmini, R. Cristofani, V. Ferrari, G. Vezzoli, M. Meroni, E. Messi, M. Piccolella, M. Galbiati, N. Ticozzi, A. Ratti, V. Silani, A.D. Carrà, I. Bigi, L. Mediani, F.F. Morelli, S. Carra, A. Poletti
TDP25 aggregation in motor neuron and muscle cells is rescued by chaperone overexpression
2018 M.E. Cicardi, R. Cristofani, P. Rusmini, M. Meroni, V. Ferrari, B. Tedesco, M. Galbiati, S. Carra, V. Crippa, A. Poletti
Trehalose induces autophagy via lysosomal-mediated TFEB activation in models of motoneuron degeneration
2018 P. Rusmini, K. Cortese, V. Crippa, R. Cristofani, M.E. Cicardi, V. Ferrari, G. Vezzoli, B. Tedesco, M. Meroni, E. Messi, M. Piccolella, M. Galbiati, M. Garrè, E. Morelli, T. Vaccari, A. Poletti
ALS-associeted VCP-mutants lead to lysosome damage
2019 V. Ferrari, M.E. Cicardi, P. Rusmini, V. Crippa, R. Cristofani, B. Tedesco, M. Galbiati, E. Messi, M. Piccolella, A. Poletti
Transcriptional alterations induced by polyDPRs overexpression in neuronal cell model
2019 ). Cristofani R., Grilli, N.V. Licata, V. Crippa, M.E. Cicardi, P. Rusmini, B. Tedesco, V. Ferrari, E. Casarotto, M. Galbiati, S. Carra, A. Provenzani, A. Poletti
Novel pathogenic mechanism of ALS-associated VCP- mutants
2019 V. Ferrari, M.E. Cicardi, P. Rusmini, V. Crippa, R. Cristofani, B. Tedesco, M. Galbiati, E. Messi, M. Piccolella, A. Poletti
The clearance of aggregated TDP-43 responsible for ALS/FTD diseases
2019 V. Crippa, M.E. Cicardi, E. Casarotto, B. Tedesco, R. Cristofani, V. Ferrari, M. Chierichetti, P. Rusmini, M. Galbiati, M. Piccolella, E. Messi, S. Carra, A. Poletti
The regulation of the small heat shock protein B8 in misfolding protein diseases causing motoneuronal and muscle cell death
2019 R. Cristofani, P. Rusmini, M. Galbiati, M.E. Cicardi, V. Ferrari, B. Tedesco, E. Casarotto, M. Chierichetti, E. Messi, M. Piccolella, S. Carra, V. Crippa, A. Poletti
Autophagic and Proteasomal Mediated Removal of Mutant Androgen Receptor in Muscle Models of Spinal and Bulbar Muscular Atrophy
2019 M.E. Cicardi, R. Cristofani, V. Crippa, V. Ferrari, B. Tedesco, E. Casarotto, M. Chierichetti, M. Galbiati, M. Piccolella, E. Messi, S. Carra, M. Pennuto, P. Rusmini, A. Poletti
C9ORF72 arginine rich poly-dipeptides induce transcriptional alterations in ALS/FTD cell model
2019 R.M. Cristofani, A. Grilli, G. Vezzoli, N. Valentina Licata, V. Crippa, M.E. Cicardi, P. Rusmini, B. Tedesco, V. Ferrari, E. Casarotto, M. Chierichetti, M. Galbiati, S. Carra, S. Bicciato, A. Provenzani, A. Poletti
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