Dermochondrocorneal dystrophy (Francois' syndrome) is an extremely rare disorder characterized by firm, nodular lesions involving the hands and the face; osteochondrodystrophy of the peripheral extremital bones, resulting in limitation of movement; and corneal dystrophy marked by white or brownish opacities. A nonfamilial case of dermochondrocorneal dystrophy was studied in a 45-year-old woman who had severe involvement of the gingival and palatal mucous membranes.
Dermochondrocorneal dystrophy (François' syndrome): report of a case / R. Caputo, N. Sambvani, M. Monti, S. Cavicchini, A. Carrassi, R. Ratiglia. - In: ARCHIVES OF DERMATOLOGY. - ISSN 0003-987X. - 124:3(1988), pp. 424-428. [10.1001/archderm.1988.01670030090029]
Dermochondrocorneal dystrophy (François' syndrome): report of a case
R. CaputoPrimo
;M. Monti;A. CarrassiPenultimo
;R. RatigliaUltimo
1988
Abstract
Dermochondrocorneal dystrophy (Francois' syndrome) is an extremely rare disorder characterized by firm, nodular lesions involving the hands and the face; osteochondrodystrophy of the peripheral extremital bones, resulting in limitation of movement; and corneal dystrophy marked by white or brownish opacities. A nonfamilial case of dermochondrocorneal dystrophy was studied in a 45-year-old woman who had severe involvement of the gingival and palatal mucous membranes.
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