The report describes a case of a newborn with a huge congenital abdominal peripheral primitive neuroectodermal tumor, with peritoneal dissemination and cutaneous involvement, and discusses literature data. Peripheral primitive neuroectodermal tumor is an exceedingly uncommon tumor in this age group and is characterized by very aggressive behavior and poor prognosis.

A case of congenital peripheral primitive neuroectodermal tumor presenting with multiple metastases / C. Meazza, A. Ferrari, M. Fumagalli, P. Collini, M. Casanova, L. Pugni, M. Colnaghi, E. Zaffignani, M. Podda, F. Mosca. - In: JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY. - ISSN 1077-4114. - 30:1(2008), pp. 36-38.

A case of congenital peripheral primitive neuroectodermal tumor presenting with multiple metastases

M. Fumagalli;M. Podda;F. Mosca
2008

Abstract

The report describes a case of a newborn with a huge congenital abdominal peripheral primitive neuroectodermal tumor, with peritoneal dissemination and cutaneous involvement, and discusses literature data. Peripheral primitive neuroectodermal tumor is an exceedingly uncommon tumor in this age group and is characterized by very aggressive behavior and poor prognosis.
Settore MED/38 - Pediatria Generale e Specialistica
Settore MED/09 - Medicina Interna
2008
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/2434/53076
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