A 47 day-old male infant, whose sudden death remained unexplained after a routine clinical and post mortem investigation, was diagnosed as SIDS. Cardiac conduction system abnormalities were found. The atrio-ventricular node appeared subdivided in two spots by the central fibrous body, configuring dual atria-ventricular pathways. The His bundle was dispersed in multiple fragments of conduction tissue, resembling the normal fetal pattern. Cartilagineous metaplasia within the central fibrous body and resorptive degeneration of the conduction tissue were also observed. These morphologic abnormalities might contribute to cardiac functional instability and possible arrhythmias.
Viene descritto ii caso di un lattante morto improvvisamente. Nel sistema di conduzione cardiaco si osservano impor tanti e rare alterazioni. Lo sdoppiamento del nodo atrio ventricolare, in particolare, potrebbe aver dato luogo a tachicardie sopraventricolari. Le anomalie descritte potrebbero costituire substrati per aritmie maligne e per morte improvvisa su base aritmogena.
Morte improvvisa del lattante : un caso di sdoppiamento del nodo atrio-ventricolare / G. Ottaviani, L. Rossi, A. Bondurri, S.G. Ramos, L. Matturri. - In: RIVISTA ITALIANA DI PEDIATRIA. - ISSN 0392-5161. - 24:6(1998), pp. 1165-1167.
Morte improvvisa del lattante : un caso di sdoppiamento del nodo atrio-ventricolare
G. Ottaviani;A. Bondurri;L. Matturri
1998
Abstract
A 47 day-old male infant, whose sudden death remained unexplained after a routine clinical and post mortem investigation, was diagnosed as SIDS. Cardiac conduction system abnormalities were found. The atrio-ventricular node appeared subdivided in two spots by the central fibrous body, configuring dual atria-ventricular pathways. The His bundle was dispersed in multiple fragments of conduction tissue, resembling the normal fetal pattern. Cartilagineous metaplasia within the central fibrous body and resorptive degeneration of the conduction tissue were also observed. These morphologic abnormalities might contribute to cardiac functional instability and possible arrhythmias.Pubblicazioni consigliate
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