We describe a unique and puzzling case of a 7-month-old baby with a non-X hypertriglyceridemic histiocytoxanthomatosis. The disease was characterized by a massive nodular eruption that was clinically, histologically, and ultrastructurally consistent with juvenile xanthogranuloma, but it had a rapid, fatal evolution.
Fatal nodular xanthomatosis in an infant / R. Caputo, E. Ermacora, C. Gelmetti, E. Gianni. - In: PEDIATRIC DERMATOLOGY. - ISSN 0736-8046. - 4:3(1987 Nov), pp. 242-246. [10.1111/j.1525-1470.1987.tb00787.x]
Fatal nodular xanthomatosis in an infant
C. GelmettiPenultimo
;
1987
Abstract
We describe a unique and puzzling case of a 7-month-old baby with a non-X hypertriglyceridemic histiocytoxanthomatosis. The disease was characterized by a massive nodular eruption that was clinically, histologically, and ultrastructurally consistent with juvenile xanthogranuloma, but it had a rapid, fatal evolution.
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