IRIS Institutional Research Information System - AIR Archivio Istituzionale della Ricerca

BARONCIANI, LUCIANO
 Distribuzione geografica
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Continente #
EU - Europa 2.265
AS - Asia 2.145
NA - Nord America 2.045
SA - Sud America 294
AF - Africa 75
OC - Oceania 7
Continente sconosciuto - Info sul continente non disponibili 1
Totale 6.832
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Nazione #
US - Stati Uniti d'America 1.943
GB - Regno Unito 748
CN - Cina 689
SG - Singapore 600
DE - Germania 343
IT - Italia 289
HK - Hong Kong 221
BR - Brasile 218
SE - Svezia 213
RU - Federazione Russa 193
VN - Vietnam 173
FR - Francia 119
BD - Bangladesh 97
IN - India 97
CA - Canada 77
NL - Olanda 68
IE - Irlanda 61
UA - Ucraina 60
FI - Finlandia 47
KR - Corea 47
JP - Giappone 46
TR - Turchia 44
CI - Costa d'Avorio 40
CO - Colombia 33
ID - Indonesia 31
ES - Italia 27
EU - Europa 20
BE - Belgio 18
IQ - Iraq 18
GR - Grecia 15
MX - Messico 15
AR - Argentina 14
CH - Svizzera 14
DK - Danimarca 14
ZA - Sudafrica 11
PK - Pakistan 10
VE - Venezuela 9
RO - Romania 8
AT - Austria 7
JO - Giordania 7
TH - Thailandia 7
MY - Malesia 6
IR - Iran 5
PH - Filippine 5
PL - Polonia 5
PY - Paraguay 5
SA - Arabia Saudita 5
AU - Australia 4
AZ - Azerbaigian 4
CL - Cile 4
LK - Sri Lanka 4
NO - Norvegia 4
PE - Perù 4
TN - Tunisia 4
UZ - Uzbekistan 4
AE - Emirati Arabi Uniti 3
CR - Costa Rica 3
EC - Ecuador 3
ET - Etiopia 3
KZ - Kazakistan 3
MA - Marocco 3
NP - Nepal 3
TW - Taiwan 3
AM - Armenia 2
BG - Bulgaria 2
BY - Bielorussia 2
DZ - Algeria 2
EG - Egitto 2
JM - Giamaica 2
NZ - Nuova Zelanda 2
PS - Palestinian Territory 2
SN - Senegal 2
UY - Uruguay 2
AO - Angola 1
BH - Bahrain 1
BO - Bolivia 1
CY - Cipro 1
CZ - Repubblica Ceca 1
EE - Estonia 1
GA - Gabon 1
GH - Ghana 1
GT - Guatemala 1
GY - Guiana 1
HN - Honduras 1
IL - Israele 1
KE - Kenya 1
KG - Kirghizistan 1
KH - Cambogia 1
KW - Kuwait 1
LB - Libano 1
LI - Liechtenstein 1
LT - Lituania 1
LY - Libia 1
MK - Macedonia 1
MT - Malta 1
NG - Nigeria 1
NI - Nicaragua 1
OM - Oman 1
PG - Papua Nuova Guinea 1
PR - Porto Rico 1
Totale 6.845
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Città #
Southend 670
Singapore 296
Ashburn 244
Frankfurt am Main 205
Hong Kong 183
San Jose 159
Beijing 125
Chandler 115
Dallas 106
Milan 80
Princeton 79
Council Bluffs 76
Seattle 70
Los Angeles 66
Dublin 59
Ho Chi Minh City 52
Ann Arbor 51
Bengaluru 49
Hefei 49
Wilmington 48
New York 47
Santa Clara 46
Jacksonville 43
Abidjan 40
Lauterbourg 40
Nanjing 40
Moscow 36
Toronto 34
Buffalo 33
Fairfield 31
Hanoi 29
Guangzhou 27
Redmond 24
Tokyo 23
Des Moines 22
Hanover 22
Jakarta 22
Rome 22
São Paulo 22
Phoenix 21
Shanghai 20
Redwood City 19
Serra 19
Seoul 18
Bogotá 17
Helsinki 17
Mountain View 17
Nanchang 17
Tianjin 17
Cambridge 15
Jinan 15
Boardman 14
Brussels 14
Cangzhou 14
Dearborn 14
Medellín 14
Montreal 14
Shenyang 14
Somerville 14
Athens 13
Da Nang 13
Houston 13
Istanbul 13
Kunming 13
Nuremberg 13
Sakarya 13
Woodbridge 13
Haiphong 12
Orem 12
Andover 11
Brooklyn 11
Hebei 11
Munich 11
Ottawa 11
Columbus 10
Naples 10
Philadelphia 10
Baghdad 9
Bitonto 9
Kent 9
London 9
Manchester 9
Amsterdam 8
Central District 8
Changsha 8
Chennai 8
Hangzhou 8
Paris 8
Roxbury 8
Salvador 8
San Diego 8
Shenzhen 8
The Dalles 8
Wuhan 8
Belo Horizonte 7
Brasília 7
Madrid 7
Norwalk 7
Stockholm 7
Washington 7
Totale 4.105
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Nome #
Severe acquired von Willebrand syndrome secondary to systemic lupus erythematosus 305
Bleeding symptoms in patients diagnosed as type 3 Von Willebrand Disease: results from 3WINTERS-IPS, an international and collaborative cross-sectional study 292
Molecular mapping of the chloride binding site in von Willebrand factor (VWF): energetics and conformational effects on the VWF/ADAMTS1-13 235
Role of von Willebrand factor in the haemostasis 226
Molecular mapping of the chloride binding site in von Willebrand factor (VWF) : energetics and conformational effects on the ADAMTS-13 interaction with wild type and type 2B R1306W VWF forms 218
The ADAMTS13-von Willebrand factor axis in COVID-19 patients 208
Genotypes of European and Iranian patients with type 3 von Willebrand disease enrolled in 3WINTERS-IPS 208
Alterata morfologia piastrinica nei pazienti con malattia di von Willebrand tipo 2B e 3 : i dati della microscopia elettronica 199
Phenotype and genotype of a cohort of families historically diagnosed with type 1 von Willebrand disease in the European study, Molecular and Clinical Markers for the Diagnosis and Management of Type 1 von Willebrand Disease (MCMDM-1VWD) 191
Mutations leading to premature termination codons in the Von Willebrand factor gene are associated with the decay of the mutant mRNAs 189
Molecular mapping of chloride binding site in VWF : energetics and conformational effects on the VWF/ADAMTS-13 interaction 189
Evaluation of the Utility of von Willebrand Factor Propeptide in the Differential Diagnosis of von Willebrand Disease and Acquired von Willebrand Syndrome 183
A two-centre comparative evaluation of new automated assays for von Willebrand factor ristocetin cofactor activity and antigen 181
A new candidate mutation, G1629R, in a patient with type 2A von Willebrand's disease: basic mechanisms and clinical implications 176
Predictors of von Willebrand disease diagnosis in individuals with borderline von Willebrand factor plasma levels 175
Evaluation of a fully automated von Willebrand factor assay panel for the diagnosis of von Willebrand disease 175
A synonymous (c.3390C>T) or a splice-site (c.3380-2A>G) mutation causes exon 26 skipping in four patients with von Willebrand disease (2A/IIE) 168
Increasing levels of von Willebrand factor and factor VIII with age in patients affected by von Willebrand disease : REPLY from original authors Biguzzi et al 168
An association of candidate gene haplotypes and bleeding severity in von Willebrand disease type 2A, 2B, and 2M pedigrees 161
The natural VWF mutant P.R1306W, causing a type 2B VWD, binds, chloride ions with lower affinity than WT VWD and is cleaved more efficently by ADAMTS-13 160
Biochemical characterization of a recombinant von Willebrand factor (VWF) with combined type 2B and type 1 defects in the VWF gene in two patients with a type 2A phenotype of von Willebrand disease 158
von Willebrand disease type 2B must be always considered in the differential diagnosis of genetic thrombocytopenias with giant platelets 156
A two-step approach (Enzyme-linked immunosorbent assay and confirmation assay) to detect antibodies against von Willebrand factor in patients with Acquired von Willebrand Syndrome 155
Molecular characterization of a multiethnic group of 21 patients with type 3 von Willebrand disease 146
Challenges and considerations of genetic testing in von Willebrand disease 145
The dominant p.Thr274Pro mutation in the von Willebrand factor propeptide causes the von Willebrand disease type 1 phenotype in two unrelated patients 144
Comparison of von Willebrand factor platelet-binding activity assays: ELISA overreads type 2B with loss of HMW multimers 143
Type 2M/2A von Willebrand disease: a shared phenotype between type 2M and 2A 135
von Willebrand factor neutralizing and non-neutralizing alloantibodies in 213 subjects with type 3 von Willebrand disease enrolled in 3WINTERS-IPS 131
Differential diagnosis between type 2A and 2B von Willebrand disease in a child with a previously undescribed de novo mutation 130
Molecular defects in type 3 von Willebrand disease: updated results from 40 multiethnic patients 123
von Willebrand disease 121
Pulmonary tumour thrombotic microangiopathy in a young man: clinical and immunohistochemical characterisation of a rare complication of gastric signet-ring cell carcinoma 116
Von Willebrand factor propeptide and pathophysiological mechanisms in European and Iranian patients with type 3 von Willebrand disease enrolled in the 3WINTERS‐IPS study 113
The type 2B p.R1306W natural mutation of von Willebrand factor dramatically enhances the multimer sensitivity to shear stress 109
An association of candidate gene haplotypes and bleeding severity in von Willebrand disease (VWD) type 1 pedigrees 105
von Willebrand disease type 1 mutation p.Arg1379Cys and the variant p.Ala1377Val synergistically determine a 2M phenotype in four Italian patients 102
Erratum to ‘A comparative study in type 2 von Willebrand disease patients using four different platelet-dependent von Willebrand factor assays.’ [Research and Practice in Thrombosis and Haemostasis Volume 7, Issue 3, March 2023, 100139] 100
Variant p.Tyr1584Cys: a frequent von Willebrand factor variant in search of von Willebrand disease 99
A comparative evaluation of a new fully automated assay for von Willebrand factor collagen binding activity to an established method 99
An international collaborative study to compare different von Willebrand factor glycoprotein Ib binding activity assays: the COMPASS-VWF study 97
Reply to “Comment on: A comparative study in type 2 von Willebrand disease patients using four different platelet-dependent von Willebrand factor assays” 96
Molecular diagnosis of von Willebrand disease 94
Emicizumab in Type 3 von Willebrand Disease: Report of a Case with an Alloantibody and Literature Review 91
How we make an accurate diagnosis of von Willebrand disease 84
Evaluation of different platelet-dependent von Willebrand factor activity assays to assess the in vivo inhibitory effect of caplacizumab on the von Willebrand factor–platelet interaction 65
null 50
Von Willebrand Disease Type 2A: An Update 33
Totale 7.147
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Categoria #
all - tutte 18.917
article - articoli 0
book - libri 0
conference - conferenze 0
curatela - curatele 0
other - altro 0
patent - brevetti 0
selected - selezionate 0
volume - volumi 0
Totale 18.917
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Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2020/2021110 0 0 0 0 0 0 0 0 0 0 75 35
2021/2022427 42 9 10 16 25 21 30 35 51 45 52 91
2022/2023651 91 64 53 53 56 101 9 30 107 25 30 32
2023/2024433 39 30 15 22 87 15 31 41 14 33 53 53
2024/20251.230 73 109 41 105 99 57 75 106 76 122 119 248
2025/20262.492 256 182 279 249 237 159 313 88 213 199 317 0
Totale 7.147