Sfoglia per Autore
Transplantation of neural stem cells derived from engineered ESC lineage (sox2-βgeo/oct4-tk cells) improves the phenotype of a mouse model of Spinal Muscular Atrophy
2009 S. Corti, M. Nizzardo, M. Nardini, S. Salani, C. Donadoni, D. Ronchi, D. Papadimitriou, R. Virgilio, N. Bresolin, G. Comi
Motoneuron transplantation rescue the phenotype of spinal muscular atrophy with respiratory distress type 1 (SMARD1)
2009 M. Nizzardo, S. Corti, M. Nardini, C. Donadoni, S. Salani, D. Ronchi, R. Del Bo, D. Papadimitriou, F. Locatelli, N. Bresolin, G.P. Comi
Motoneurons transplantation with pharmacological therapy to promote axonal elongation improves the phenotype of a model of Spinal Muscolar Atrophy with Respiratory Distress Type 1 (SMARD1)
2009 S. Corti, M. Nizzardo, M. Nardini, C. Donadoni, R. Del Bo, D. Papadimitriou, F. Locatelli, N. Mezzina, N. Bresolin, G.P. Comi
The mitochondrial disulfide relay system protein GFER is mutated in sutosomal-tecessive myopathy with vataract and vombined respiratory-chain deficiency
2009 A.B. Di Fonzo, D. Ronchi, T. Lodi , E. Fassone, M. Tigano, C. Lamperti, S.P. Corti, A. Bordoni, F.R. Fortunato, M. Nizzardo, L. Napoli, C. Donadoni, S. Salani, F. Saladino, M. Moggio, N. Bresolin, I. Ferrero, G.P. Comi
Motoneuron transplantation rescues the phenotype of spinal muscular atrophy with respiratory distress type 1
2009 S. Corti, M. Nizzardo, M. Nardini, C. Donadoni, S. Salani, R. Del Bo, D. Papadimitriou, F. Locatelli, N. Bresolin, G.P. Comi
The mitochondrial disulfide relay system protein GFER is mutated in autosomal recessive myopathy with congenital cataract and COX deficiency
2009 A. Di Fonzo, D. Ronchi, T. Lodi, E. Fassone, M. Tingano, C. Lamperti, S. Corti, A. Bordoni, F. Fortunato, M. Nizzardo, L. Napoli, C. Donadoni, S. Salani, M. Moggio, N. Bresolin, I. Ferrero, G. Comi
Neural stem cells derived from genetically engineered lineage-selectable Es cells improves the phenotype of a mouse model of spinal muscular atrophy
2009 S. Corti, M. Nizzardo, S. Salani, M. Nardini, C. Donadoni, C. Simone, M. Falcone, N. Bresolin, G.P. Comi
The mitochondrial disulfide relay system protein GFER is mutated in autosomal recessive myopathy with congenital cataract and COX deficiency.
2009 A. Di Fonzo, D. Ronchi, T. Lodi, E. Fassone, M. Tigano, C. Lamperti, S. Corti, A. Bordoni, F. Fortunato, M. Nizzardo, L. Napoli, C. Donadoni, S. Salani, M. Moggio, N. Bresolin, I. Ferrero, G.P. Comi
Transplantation of neural stem cells derived from genetically engineered, lineage-selectable ES cells improves spinal muscular atrophy
2009 M. Nizzardo, S. Salani, M. Nardini, C. Donadoni, D. Ronchi, C. Simone, M. Falcone, N. Bresolin, G.P. Comi, S. Corti
Stem Cell-derived motoneurons rescue the phenotype of spinal muscular atrophy with respiratory distress type 1 (SMARD1)
2009 S. Corti, M. Nizzardo, M. Nardini, C. Donadoni, S. Salani, R. Del Bo, D. Papadimitriou, F. Locatelli, N. Bresolin, G.P. Comi
Motoneuron Transplantation Rescues the Phenotype of SMARD1 (Spinal Muscular Atrophy with Respiratory Distress Type 1)
2009 S. Corti, M. Nizzardo, M. Nardini, C. Donadoni, S. Salani, R. Del Bo, D. Papadimitriou, F. Locatelli, N. Mezzina, F. Gianni, N. Bresolin, G.P. Comi
Pluripotent engineered stem cell-derived neural stem cells improve spinal muscular atrophy phenotype in mice
2009 M. Nizzardo, M. Nardini, S. Salani, C. Donadoni, C. Simone, M. Falcone, N. Mezzina, F. Gianni, D. Ronchi, D. Papadimitriou, N. Bresolin, G. Comi, S.P. Corti
Beta-lactam antibiotic offer neuroprotection in a spinal muscular atrophy mouse model by multiple mechanisms
2010 M. Nizzardo, M. Nardini, D. Ronchi, S. Salani, C. Simone, M. Falcone, C. Donadoni, G.P. Comi, S.P. Corti
Systemic transplantation of c-kit+ cells exerts a therapeutic effect in a model of Amyotrophic Lateral Sclerosis
2010 S. Corti, M. Nizzardo, M. Nardini, C. Donadoni, S. Salani, C. Simone, M. Falcone, N. Mezzina, F. Gianni, G. Riboldi, N. Bresolin, G.P. Comi
Systemic transplantation of c-kit+ cells exerts a therapeutic effect in a model of Amyotrophic Lateral Sclerosis
2010 S. Corti, M. Nizzardo, M. Nardini, C. Donadoni, S. Salani, C. Simone, M. Falcone, G. Riboldi, N. Bresolin, G.P. Comi
Systemic transplantation of c-kit+ cells exerts a therapeutic effect in a model of Amyotrophic Lateral Sclerosis
2010 S. Corti, M. Nizzardo, M. Nardini, C. Donadoni, S. Salani, C. Simone, M. Falcone, N. Mezzina, F. Gianni, G. Riboldi, N. Bresolin, G.P. Comi
Beta lactam antibiotic ameliorates spinal muscular atrophy phenotype in a mouse model by multiple mechanisms
2010 S. Corti, M. Nizzardo, M. Nardini, C. Donadoni, S. Salani, C. Simone, M. Falcone, G. Riboldi, N. Bresolin, G.P. Comi
Systemic transplantation of c-kit+ cells can ameliorate the phenotype of a mouse model of Amyotrophic Lateral Sclerosis
2010 S. Corti, M. Nizzardo, M. Nardini, C. Donadoni, S. Salani, C. Simone, M. Falcone, G. Riboldi, N. Bresolin, G.P. Comi
Systemic transplantation of c-kit+ cells exerts a therapeutic effect in a model of amyotrophic lateral sclerosis
2010 S. Corti, M. Nizzardo, M. Nardini, C. Donadoni, S. Salani, C. Simone, M. Falcone, G. Riboldi, A. Govoni, N. Bresolin, G.P. Comi
Embryonic stem cell–derived neural stem cells improve spinal muscular atrophy phenotype in mice
2010 S.P. Corti, M. Nizzardo, M. Nardini, C. Donadoni, S. Salani, D. Ronchi, C. Simone, M. Falcone, D. Papadimitriou, F. Locatelli, N. Mezzina, F. Gianni, N. Bresolin, G.P. Comi
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