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Titolo Data di pubblicazione Autori Tipo File Abstract
The small heat shock protein B8 (HSPB8) efficiently removes aggregating species of dipeptides produced in C9ORF72-related neurodegenerative diseases 2017 R. CristofaniV. CrippaP. RusminiM. GalbiatiM.E. CicardiM. MeroniV. FerrariB. TedescoM. PiccolellaE. MessiA. Poletti + Article (author) -
Autophagy mediated HSPB8 removal of aggregating dipeptides produced in C9ORF72 related neurodegenerative diseases 2017 R. CristofaniP. RusminiM. GalbiatiM.E. CicardiM. MeroniV. FerrariB. TedescoV. CrippaA. Poletti + Conference Object -
The Role of the Heat Shock Protein B8 (HSPB8) in Motoneuron Diseases 2017 P. RusminiR. CristofaniM. GalbiatiM.E. CicardiM. MeroniV. FerrariB. TedescoE. MessiM. PiccolellaV. CrippaA. Poletti + Article (author) -
The role of Valosin Containing Protein (VCP) in the degradation of neurotoxic protein aggregates in Amyotrophic Lateral Sclerosis 2017 V. FerrariM.E. CicardiV. CrippaP. RusminiR. CristofaniM. MeroniG. VezzoliB. TedescoA. Poletti + Conference Object -
Effects of mutations of the pro-autophagic protein Heat Shock Protein B8 in motoneuron disease 2017 tedesco barbaracrippa valeriarusmini paolacristofani riccardocicardi maria elenaferrari veronicameroni marcomessi eliopiccolella margheritagalbiati ritapoletti angelo + Conference Object -
The chaperone HSPB8 removes insoluble forms of the C9ORF72 RAN translated dipeptides responsible for ALS/FTD 2017 R. CristofaniG. VezzoliP. RusminiM. GalbiatiM. E. CicardiM. MeroniV. FerrariB. TedescoV. CrippaA. Poletti + Conference Object -
Clearance of misfolded proteins in motoneuron disease: the case of Spinal and Bulbar Muscular Atrophy 2017 P. RusminiV. CrippaM. MeroniR. CristofaniB. TedescoV. FerrariM. GalbiatiA. Poletti + Conference Object -
The role of protein quality control system in Amyotrophic Lateral Sclerosis 2017 V. CrippaR. CristofaniM. E. CicardiP. RusminiV. FerrariG. VezzoliB. TedescoM. MeroniM. GalbiatiA. Poletti Conference Object -
Tdp-25 Routing to Autophagy and Proteasome Ameliorates its Aggregation in Amyotrophic Lateral Sclerosis Target Cells 2018 Cicardi, Maria ElenaCristofani, RiccardoRusmini, PaolaMeroni, MarcoFerrari, VeronicaTedesco, BarbaraPiccolella, MargheritaMessi, ElioGalbiati, MariaritaBoncoraglio, AlessandraCrippa, ValeriaPoletti, Angelo + Article (author) -
Characterization of two new mutations in the small Heat Shock protein B8 HSPB8 and impact in Amyotrophic Lateral Sclerosis cell models 2018 barbara tedescovaleria cripparusmini paolacristofani riccardocicardi maria elenaferrari veronicameroni marcomessi eliopiccolella margheritagalbiati ritapoletti angelo + Conference Object -
Novel role of VCP in the clearance of mutant-SOD1 in als 2018 Ferrari V.Cicardi M. E.Crippa V.Rusmini P.Cristofani R.Meroni M.Tedesco B.Galbiati M.Poletti A. Conference Object -
VCP: a novel regulator of SOD1-G93A clearance in a als model 2018 Ferrari V.Cicardi M. E.Crippa V.Rusmini P.Cristofani R.Meroni M.Tedesco B.Galbiati M.Poletti A Conference Object -
New HSPB8 mutations related to Amyotrophic Lateral Sclerosis : characterization and impact in cell models of disease 2018 tedesco barbaracrippa valeriarusmini paolacristofani riccardocicardi maria elenaferrari veronicameroni marcomessi eliopiccolella margheritagalbiati ritapoletti angelo + Conference Object -
Chaperone Assisted Selective Autophagy (CASA) a potential target for therapeutics in motoneuron diseases 2018 Crippa V.Rusmini P.Cristofani R.Cicardi M. E.Meroni M.Ferrari V.Tedesco B.Piccolella M.Messi E.Galbiati M.Poletti A. Conference Object -
Chaperone mediated autophagy respond to dynein mediated transport inhibition in motor neuron diseases 2018 Riccardo CristofaniValeria CrippaMaria Elena CicardiPaola RusminiMarco MeroniVeronica FerrariTEDESCO, BARBARAMariarita GalbiatiAngelo Poletti + Conference Object -
Pro209 mutations on the Bcl-2-Associated Athanogene 3 BAG3 : common molecular behaviors of mutants linked to distinct diseases 2018 tedesco barbaravaleria crippaangelo poletti + Conference Object -
The small heat shock protein B8 at the interplay between the intracellular degradative pathways in motoneuron disease 2018 A. POLETTIR. CRISTOFANIV. CRIPPAP. RUSMINIV. FERRARIB. TEDESCOM. MERONIM. GALBIATI + Conference Object -
Chaperone mediated autophagy responds to macroautophagy inhibition in motor neuron diseases 2018 Riccardo CristofaniValeria CrippaMaria Elena CicardiPaola RusminiMarco MeroniVeronica FerrariBarbara TedescoMariarita GalbiatiElio MessiMargherita PiccolellaAngelo Poletti + Conference Object -
The small heat shock protein B8 (HSPB8) removes dipeptides produced in C9ORF72-related neurodegenerative diseases 2018 Cristofani RCrippa VCicardi MERusmini PMeroni MFerrari VTedesco BMessi EPiccolella MGalbiati MPoletti A + Conference Object -
Identification of new HSPB8 variants linked to familial Amiotrophic Lateral Sclerosis 2018 V. CrippaB. TedescoM. E. CicardiP. RusminiR. CristofaniV. FerrariM. MeroniE. MessiM. PiccolellaM. GalbiatiN. TicozziA. RattiV. SilaniA . Poletti + Conference Object -
Mostrati risultati da 1 a 20 di 96
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